(IV – 2A.1; IV – 5A.2) Patient with congenital heart desease – Tetralogy of Fallot – after surgical correction and with severe pulmonic valve regurgitation and moderate tricuspid valve regurgitation
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV – 2A.1) Patient after operation of tetralogy of Falot with patent blalock – Taussig Natalia Dłużniewska MD; dr n. med. Lidia Tomkiewicz – Pająk MD, Jakub Stępniewski; PhD; prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV- 2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Piotr Podolec Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT Despite the lack of symptoms there is a significant leakage, reduced contractility of the left and right ventricle and the pulmonary artery trunk extension. It seems reasonable to close of atrial septal defect – to consider is the choice of method (percutaneous using Amplatz device or surgical, which additional advantage is a possibility of leaving a little septal communication …
(IV-2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Krzysztof Szymoński, MD Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland COMMENT Regarding whole clinical presentation biological pulmonary valve replacement and tricuspid valvuloplasty seems appropriate, especially taking into account that the patient is planning pregnancy. Concomitant right ventricular plasty may also be considered. CONCLUSIONS Regarding the patient is planning pregnancy, biological pulmonary valve replacement together with tricuspid valvuloplasty seems reasonable, concomitant right ventricular plasty may also be considered. “Development of the …
(IV-2A.1 ) Adult patient with Tetralogy of Fallot after Blalock-Taussing anastomosis Agnieszka Żygadło MD, Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, PhD, Monika Smaś-Suska MD, Natalia Dłużniewska MD, Joanna Łuszczak MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski, MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT There are indications for surgical intervention. However, heart catheterisation should be performed in the first place. Optimal management would be VSD and shunt closure, and creating communication between atria. Minimal ventriculotomy may also be considered. EXPERT: Prof. Zbigniew Kordon, MD, PhD Affiliation: Department of Pediatric Cardiology, Jagiellonian University Medical College, Krakow, Poland COMMENT Pulmonary hypertension is suspected in …
(IV-2A.1) Patient after total correction of Tetralogy of Fallot with syncope Magdalena Kostkiewicz MD, PhD, Sylwia Wiśniowska-Śmiałek MD, Agata Leśniak-Sobelga MD,PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Tomasz Miszalski-Jamka, MD, PhD Affiliation: Department of Radiology, John Paul II Hospital, Krakow, Poland COMMENT In CMR impaired RV contractility can be seen. Additionally pulmonary valve stenosis, accelerated blood flow and right pulmonary artery dilatation is present. Gradient in ostium is about 20 mmHg. There is no visible fibrosis in RV muscle. EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow COMMENT In this particular case residual heart …
(IV-2A.1) Patient with Tetralogy of Fallot after surgery with VSD, pulmonary hypertension and symptoms of heart failure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD. PhD, Prof. Maria Olszowska MD. PhD, Prof. Piotr Podolec MD, PhD.
Background Tetralogy of Fallot is a congenital cardiac malformation that consists of an interventricular communication, also known as a ventricular septal defect, obstruction of the right ventricular outflow tract, override of the ventricular septum by the aortic root, and right ventricular hypertrophy. Case presentation A 40-year-old woman after correction of tetralogy of Fallot (ToF) was admitted to hospital due to deterioration in exercise tolerance (NYHA functional class III). Surgical correction was performed at the age of 3 years. She was …
(IV-2A.1) Uncorrected Tetralogy of Fallot and Ischemic Heart Disease in a 57 Years Old Man prof.E.Ereminienė; prof. J. Vaškelytė; res.R.Ordienė; res.B.Kaminskaitė; res.T.Lapinskas; E.Kazakauskaitė
Background Tetralogy of Fallot (ToF), first described in 1888, comprises of an interventricular septal defect, right ventricular outflow tract obstruction, an overriding aorta, and right ventricular hypertrophy (RVH). It is the most common form of cyanotic congenital heart disease (10% of all cases). It is usually detected in early infancy due to symptoms related to cyanosis and right to left shunting of blood through a large ventricular septal defect. Uncorrected, it is associated with a very poor prognosis, with only …
(IV-2A.1) 43-year-old patient with unoperated Tetralogy of Fallot (ToF) lek. Agnieszka Sikora-Puz, dr n.med. Maciej Haberka, dr n.med. Leszek Szymański, lek. Piotr Pysz, prof. dr hab. n. med. Zbigniew Gąsior
Background Tetralogy of Fallot is a congenital cyanotic heart defect composed of four characteristics: large ventricular septal defect (VSD) – malaligment type, overriding aorta, right ventricular hypertrophy and right ventricular outflow obstruction. The location of the obstruction can be anywhere along the right ventricular outflow-infundibulum, pulmonic valve, the annulus of the pulmonic valve, the main pulmonary arteria (PA), or in the branch or peripheral pulmonary arteries. The degree of obstruction in the right ventricle outflow truck can range mild to …