(IV – 2A.1; IV – 5A.2) Patient with congenital heart desease – Tetralogy of Fallot – after surgical correction and with severe pulmonic valve regurgitation and moderate tricuspid valve regurgitation
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5.A2) An 18-year-old patient after baloon aortic valvuloplasty with severe aortic regurgitation and pulmonary hypertension Paweł Prochownik, Monika Komar, Bartosz Sobień, Urszula Gancarczyk, Natasza Herman, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5A.2) Adult patient with common artery truncus and RV-PA conduit stenosis Lidia Tomkiewicz-Pająk MD, PhD , Prof. Maria Olszowska MD, PhD, Monika Komar MD, PhD, Prof. Piotr Podolec MD, PhD Grzegorz Kopeć MD, PhD, Jakub Podolec MD.
Background Truncus arteriosus communis (TAC) is a rare congenital heart disease appearing in 0.034 to 0.56 per 1,000 newborns and representing 1.4% to 2.8% of all cases of congenital heart disease . In this anomaly, a single arterial trunk arises from the heart, overrides the interventricular septum, and supplies systemic, pulmonary, and coronary circulations. Without surgical treatment, 80% of patients die within the first year of life, usually in early infancy. Repair of TAC during the neonatal and early infant …
(IV-5A.2) Adult patient with endocarditis after the Ross-Konno procedure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, Maria Olszowska MD, PhD, Grzegorz Kopeć MD, PhD
Background The Ross procedure is a type of valve surgery where the patient’s pulmonary valve is removed and switched to the aortic position. In the pulmonary position , a homograft is placed. The Konno modification of the Ross procedure allows an autograft aortic valve replacement in children with annular and subannular hypoplasia. The Ross-Konno procedure enables potential for growth of the pulmonary autograft in the aortic position. The lifelong anticoagulation can be avoided [1,2]. Meta-analysis of thirty-nine studies (n=5031) shows …
(IV-5A.2) Patient with stenotic conduit after surgical correction of Tetralogy of Fallot Dawid Kudliński MD, Magdalena Kostkiewicz MD, PhD, Agata Leśniak-Sobelga MD, Lidia Tomkiewicz-Pająk MD, PhD, Tomasz Miszalski-Jamka MD, PhD, Prof. Piotr Podolec MD, PhD
Background Tetralogy of Fallot is a one of congenital heart defects involving four anatomical abnormalities: pulmonary stenosis or pulmonary atresia, overriding aorta, ventricular septal defect, right ventricular hypertrophy. It is the most common cyanotic heart defect. The main symptoms are a bluish coloration of the skin caused by blood low in oxygen (cyanosis), a heart murmur and clabbing of fingers. Tetralogy of Fallot with atresia of the left pulmonary artery is presented by 10% of patients. Case presentation We present …
(IV-5A.2) Patient with significant pulmonary valve regurgitation after Fallot operation Lidia Tomkiewicz-Pająk MD. PhD., Maria Olszowska MD. PhD., Prof. Piotr Podolec MD. PhD.
Background Tetralogy of Fallot (ToF) is the cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently present complications. They include: severe pulmonary regurgitation, right ventricular outflow tract obstruction, right ventricular dilation and dysfunction, residual …
(IV-5A.2) Patient after correction of Tetralogy of Fallot with pulmonary valve regurgitation and left pulmonary branch stenosis Tomkiewicz-Pająk L. MD, PhD, Podolec J. MD, Kopeć G. MD, PhD, Drabik L. MD, Assoc. Prof. Olszowska M. MD, PhD, Miszalski-Jamka T. MD, PhD, Assoc. Prof. Kostkiewicz M. MD, PhD, Tyrka A. MD
Keywords: correction of Tetralogy, pulmonary valve regurgitation, left pulmonary branch stenosis Background Tetralogy of Fallot (ToF) is a cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently develop complications such as severe pulmonary regurgitation, …