(IV-1C.3a, IV-2A.O) 38-year old female patient with a congenitally corrected transposition of the great arteries Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Maria Olszowska, Piotr Podolec
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-1C.3a, V-2B.O ) 25 – year old patient with a transposition of the great arteries and arrhythmia Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Paweł Iwaszczuk, Maria Olszowska, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
Posted in – Others, 1. Abnormalities of the position and connection of the heart and vessels, 2. Arrhythmias secondary to rare structural diseases of the heart, 3. Great arteries, B. Due to congenital heart diseases, C. Veins and arteries, Case presentations, IV. Rare congenital cardiovascular diseases, V. Rare arrhythmias
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(IV-1D.2d) 21-year old patient with bicuspid aortic valve Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Natalia Dłużniewska, Maria Olszowska, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1) Heart failure in Fontan patient Lidia Tomkiewicz-Pająk, Monika Smaś –Suska, Maria Olszowska, Wojciech Płazak, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1) 31-year old patient after Fontan operation with systemic AV valve regurgitation Knap K. MD, Tomkiewicz- Pająk L. MD, PhD, Prof. Olszowska M. MD, PhD, Prof. Podolec P. MD, PhD, Smaś- Suska M. MD, Jurkowska- Błaut J. MD
EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
( I – 2A.0; IV – 1D.2d ) Patient with artificial aortic valve with aneurysm of ascending aorta Natalia Dłużniewska MD; Lidia Tomkiewicz – Pająk MD, PhD; Aleksandra Lenart MD, Monika Smaś – Suska MD, Prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD, pediatric cardiac surgeon Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT Ascending aorta’s diameter has shown widening tendency. It is difficult to determine if the implanted AV is still suitable for the patient. I recommend consideration of AVR procedure (for example implantation of biological valve and plasty of the ascending aorta). Bioprothesis might improve the patient’s quality of life. Aortic homograft implantation would make possible …
Posted in 1. Abnormalities of the position and connection of the heart and vessels, 2. Connective tissue disorders causing aneurysmal disease, 2. Left heart valves, A. Aneurysmal disease of the aorta, Case presentations, D. Valves, I. Rare diseases of systemic circulation, IV. Rare congenital cardiovascular diseases, Others
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(IV-1C.3/II-2A.1) 41-year old patient with arterial pulmonary hypertension and unilateral pulmonary artery absence Blaszczak Piotr MD PhD, Grzywna Ryszard MD PhD, Gorczyca Daria MD, Siudak Łukasz MD
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
Posted in 1. Abnormalities of the position and connection of the heart and vessels, 1. Atresia of the pulmonary artery, 2. Inborn anomalies of the pulmonary vessels, 3. Great arteries, A. Anomalous morphology, C. Veins and arteries, Case presentations, II. Rare diseases of pulmonary circulation, IV. Rare congenital cardiovascular diseases
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(IV-2B.1, IV-4D) Patient with thrombophilia after the episode of deep vein thrombosis of lower extremity with insignificant ASD Danuta Sorysz MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-2B.1) 57-year-old woman with Eisenmenger’s syndrome and ischemic stroke in anamnesis Joanna Stanisz-Kempa MD Małgorzata Biedroń MD Assoc. Prof. Józefa Dąbek MD, PhD Prof. Zbigniew Gąsior MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-3.B) Long-term survival in unoperated double-inlet ventricle M. Haberka, M. Biedroń, E. Jastrzębska-Maj, L. Szymański, K. Bańska, M. Skowerski, Z. Gąsior
BRIEF COMMENTS EXPERT: Prof. Henryk Siniawski MD, PhD, cardiac surgeon Affiliation: German Heart Instiute, Berlin, Germany COMMENT I would recommend RHC in order to exclude pulmonary hypertension. Optimal medical treatment is necessary to protect the patient form cardiac decompensation in the future. EXPERT: Assoc. Prof. Jacek Pająk, MD, PhD, pediatric cardiac surgeon Affiliation: Silesian Center for Heart Diseases, Zabrze, Poland COMMENT It appears that conservative treatment and watchful observation would be the most reasonable proceeding. EXPERT: Assoc. Prof. Jacek …