(IV-1C.3a, IV-2A.O) 38-year old female patient with a congenitally corrected transposition of the great arteries Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Maria Olszowska, Piotr Podolec

  “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

Posted in – Others, 1. Abnormalities of the position and connection of the heart and vessels, 2. Shunts, 3. Great arteries, A. Decreased pulmonary flow, C. Veins and arteries, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV – 2A.1; IV – 5A.2) Patient with congenital heart desease – Tetralogy of Fallot – after surgical correction and with severe pulmonic valve regurgitation and moderate tricuspid valve regurgitation

“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

Posted in 1. Tetralogy of Fallot, 2. Postprocedural complication and residual defects, 2. Shunts, 5. Grown-up congenital cardiovascular diseases, A. After correction, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV – 2A.1) Patient after operation of tetralogy of Falot with patent blalock – Taussig Natalia Dłużniewska MD; dr n. med. Lidia Tomkiewicz – Pająk MD, Jakub Stępniewski; PhD; prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD

  EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV- 2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

  BRIEF COMMENTS EXPERT: Prof. Piotr Podolec Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT Despite the lack of symptoms there is a significant leakage, reduced contractility of the left and right ventricle and the pulmonary artery trunk extension. It seems reasonable to close of atrial septal defect – to consider is the choice of method (percutaneous using Amplatz device or surgical, which additional advantage is a possibility of leaving a little septal communication …

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

  BRIEF COMMENTS EXPERT: Krzysztof Szymoński, MD Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland COMMENT Regarding whole clinical presentation biological pulmonary valve replacement and tricuspid valvuloplasty seems appropriate, especially taking into account that the patient is planning pregnancy. Concomitant right ventricular plasty may also be considered. CONCLUSIONS Regarding the patient is planning pregnancy, biological pulmonary valve replacement together with tricuspid valvuloplasty seems reasonable, concomitant right ventricular plasty may also be considered. “Development of the …

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.1 ) Adult patient with Tetralogy of Fallot after Blalock-Taussing anastomosis Agnieszka Żygadło MD, Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, PhD, Monika Smaś-Suska MD, Natalia Dłużniewska MD, Joanna Łuszczak MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

  BRIEF COMMENTS EXPERT: Prof. Janusz Skalski, MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT There are indications for surgical intervention. However, heart catheterisation should be performed in the first place. Optimal management would be VSD and shunt closure, and creating communication between atria. Minimal ventriculotomy may also be considered. EXPERT: Prof. Zbigniew Kordon, MD, PhD Affiliation: Department of Pediatric Cardiology, Jagiellonian University Medical College, Krakow, Poland COMMENT Pulmonary hypertension is suspected in …

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.1) Patient after operation of Tetralogy of Fallot Lidia Tomkiewicz-Pająk MD PhD, , PhD, Natalia Dłużniewska MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.3) An adult patient with a single ventricle Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Maria Olszowska, Piotr Podolec

  BRIEF COMMENTS EXPERT: Lidia Tomkiewicz-Pająk MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow COMMENT In my opinion Fontan procedure wouldn’t be suitable for this patient. There is a significant tricuspid regurgitation, function of single ventricle wouldn’t be sufficient after Fontan operation. The best option is heart transplantation. EXPERT: Prof. Lesław Szydłowski MD, PhD Affiliation: 1st Department of Paediatric Cardiology, Medical University of Silesia, Katowice-Ligota, Poland COMMENT In case of significant tricuspid regurgitation Fontan …

Posted in 2. Shunts, 3. Pulmonary atresia and ventricular septal defect, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.1) Patient after total correction of Tetralogy of Fallot with syncope Magdalena Kostkiewicz MD, PhD, Sylwia Wiśniowska-Śmiałek MD, Agata Leśniak-Sobelga MD,PhD, Prof. Piotr Podolec MD, PhD

  BRIEF COMMENTS EXPERT: Tomasz Miszalski-Jamka, MD, PhD Affiliation: Department of Radiology, John Paul II Hospital, Krakow, Poland COMMENT In CMR impaired RV contractility can be seen. Additionally pulmonary valve stenosis, accelerated blood flow and right pulmonary artery dilatation is present. Gradient in ostium is about 20 mmHg. There is no visible fibrosis in RV muscle. EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow COMMENT In this particular case residual heart …

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-2A.1) Patient with Tetralogy of Fallot after surgery with VSD, pulmonary hypertension and symptoms of heart failure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD. PhD, Prof. Maria Olszowska MD. PhD, Prof. Piotr Podolec MD, PhD.

Background Tetralogy of Fallot is a congenital cardiac malformation that consists of an interventricular communication, also known as a ventricular septal defect, obstruction of the right ventricular outflow tract, override of the ventricular septum by the aortic root, and right ventricular hypertrophy. Case presentation A 40-year-old woman after correction of tetralogy of Fallot (ToF) was admitted to hospital due to deterioration in exercise tolerance (NYHA functional class III). Surgical correction was performed at the age of 3 years. She was …

Posted in 1. Tetralogy of Fallot, 2. Shunts, A. Decreased pulmonary flow, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment