BRIEF COMMENTS
EXPERT: Prof. Janusz Skalski, MD, PhD
Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland
COMMENT
There are indications for surgical intervention. However, heart catheterisation should be performed in the first place. Optimal management would be VSD and shunt closure, and creating communication between atria. Minimal ventriculotomy may also be considered.
EXPERT: Prof. Zbigniew Kordon, MD, PhD
Affiliation: Department of Pediatric Cardiology, Jagiellonian University Medical College, Krakow, Poland
COMMENT
Pulmonary hypertension is suspected in this patient. Due to complex anatomy the most optimal management would be decompression on the level of atria. It is a large intervention. Placing a stent into pulmonary artery may also be considered.
EXPERT: Assoc. Prof. Bogusław Kapelak, MD, PhD
Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland
COMMENT
In this patient the risk associated with surgery is approx. 10%. Before surgery heart catheterisation should be performed and risk reestimated. Proposed intervention would consist of ventricular septal defect and shunt closure, and creating communication between atria.
EXPERT: Prof. Lesław Szydłowski, MD, PhD
Affiliation: 1st Department of Paediatric Cardiology, Medical University of Silesia, Katowice-Ligota, Poland
COMMENT
Despite patient’s age, the clinical course of the disease promotes surgical intervention.
CONCLUSIONS
1. Surgical treatment is possible.
2. If the patient gives consent for proposed intervention, preceding heart catheterisation followed by requalification is indicated.
3. Current estimated risk associated with surgery is approx. 10%. Patient should be informed about the extend and technique of intervention as well as the risk and expected results.
4. Prophylaxis of infectious endocarditis is recommended.
“Development of the European Network in Orphan Cardiovascular Diseases”
„Rozszerzenie Europejskiej Sieci Współpracy ds Sierocych Chorób Kardiologicznych”
