(IV-2A.1) Adult patients with Fallot Syndrom Lidia Tomkiewicz- Pajak MD., PhD., Joanna Luszczak MD., Prof. Piotr Podolec MD., PhD.
Background Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart disease. It is caused by the antero-supetior displacement of the infundibular septum what leads to the onset of the components of the ToF: malaligned ventricular septal defect (VSD), overriding aorta, right ventricular outflow tract obstruction (RVOTO) and, secondary, right ventricle (RV) hypertrophy. Uncorrected ToF has short life expectancy- about 25% of patients survive to age of 10 years and only 5% to age of 40 years[1,2]. However, long-term …
(IV-6.1) Double-chambered left ventricle in a young previously healthy man presenting for a routine echocardiographic study Katarzyna Mizia-Stec MD, PhD, Prof., Tomasz Bochenek MD, PhD, Magdalena Mizia MD, PhD
Background A double-chambered left ventricle (DCLV) constitutes a rare congenital malformation. It is usually diagnosed at a neonatal or pediatric age, and often exhibits mixed criteria for diverticulae and aneurysms. This anomaly is characterized by the subdivision of the left ventricle into two chambers by an abnormal septum or muscle band. In this article, we present the case of 30-year-old asymptomatic patient, in whom DCLV was diagnosed by routine echocardiographic study. Case presentation We present the case report of a …
(IV-5A.2) Patient with stenotic conduit after surgical correction of Tetralogy of Fallot Dawid Kudliński MD, Magdalena Kostkiewicz MD, PhD, Agata Leśniak-Sobelga MD, Lidia Tomkiewicz-Pająk MD, PhD, Tomasz Miszalski-Jamka MD, PhD, Prof. Piotr Podolec MD, PhD
Background Tetralogy of Fallot is a one of congenital heart defects involving four anatomical abnormalities: pulmonary stenosis or pulmonary atresia, overriding aorta, ventricular septal defect, right ventricular hypertrophy. It is the most common cyanotic heart defect. The main symptoms are a bluish coloration of the skin caused by blood low in oxygen (cyanosis), a heart murmur and clabbing of fingers. Tetralogy of Fallot with atresia of the left pulmonary artery is presented by 10% of patients. Case presentation We present …
(IV-2A.3) Ventricular septal defect and pulmonary atresia Agnieszka Sarnecka MD, Grzegorz Kopeć MD. PhD, Prof. Piotr Podolec MD. PhD
Background Pulmonary atresia with ventricular septal defect (PA + VSD) is a cyanotic congenital heart disease, also called Tetralogy of Fallot with pulmonary atresia. The intracardiac anatomy is similar to tetralogy but there is no direct communication between the right ventricle and pulmonary arteries. Major problems with surgical treatment are related to complexity of the pulmonary vascular bed that may make repair impossible. Case presentation We present a case of a 50-year old woman with congenital heart disease who was …
(IV-3B) The patient with TGA, VSD, PS after Rastelli procedure Lidia Tomkiewicz-Pająk MD. PhD., Maria Olszowska MD. PhD., Prof. Piotr Podolec MD. PhD.
Background Transposition of the great vessels is a congenital cyanotic heart defect. The hallmark of transposition of the great arteries is ventriculoarterial discordance, in which the aorta arises from the morphologic right ventricle and the pulmonary artery arises from the morphologic left ventricle. The Rastelli operation is performed for the repair of d-transposition of the great vessels with ventricular septal defect and pulmonary stenosis. During the surgery right ventricular outflow truckt – pulmonary arteries conduit is implanted and VSD is …
(IV-1C.3.o) Patient with Taussig-Bing syndrome Drabik L., MD, Tomkiewicz-Pająk L., MD, PhD, Prof. Olszowska M., MD, PhD, Prof. Podolec P., MD, PhD
Background Taussig-Bing syndrome is a rare congenital heart malformation consisting of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect. Taussig-Bing syndrome is frequently associated with other cardiac abnormalities: right ventricular outflow tract obstruction, aortic arch obstruction and unusual coronary pattern [1].There are essential differences between Taussig-Bing syndrome and transposition of the great arteries with ventricular septal defect and overriding pulmonary artery. Taussig-Bing syndrome is characterized by true double-outlet right …
(IV-5A.2) Patient with significant pulmonary valve regurgitation after Fallot operation Lidia Tomkiewicz-Pająk MD. PhD., Maria Olszowska MD. PhD., Prof. Piotr Podolec MD. PhD.
Background Tetralogy of Fallot (ToF) is the cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently present complications. They include: severe pulmonary regurgitation, right ventricular outflow tract obstruction, right ventricular dilation and dysfunction, residual …
(IV-2A.1) 56 -year-old male with Tetralogy of Fallot Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, Maria Olszowska MD, PhD, Prof. Piotr Podolec Md, PhD
Background Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart disease. It is caused by the antero-superior displacement of the infundibular septum what leads to the onset of the components of the ToF: malaligned ventricular septal defect (VSD), overriding aorta, right ventricular outflow tract obstruction (RVOTO) and, secondary, right ventricle (RV) hypertrophy. Uncorrected ToF has short life expectancy- about 25% of patients survive to age of 10 years and only 5% to age of 40 years[1,2]. However, long-term …
(IV-1D.1b) Patient with Ebstein anomaly, VSD and heart failure Prof. Andrzej Gackowski MD, PhD, Anton Chrustowicz MD, PhD
Background Ebstein anomaly is a rare congenital defect. Tricuspid valve in these patients is displaced towards the apex of the right ventricle. As a result part of the right ventricular muscle is located in functional atrium and the right ventricular volume is decreased comparing to normal. Depending on the degree of valve malformation and RV atrialisation different clinical presentation is possible – from mild symptoms to severe right heart failure. Case presentation We present a case of 35-years old lady …
(IV-4D) Patient with PFO and thrombophilia after ischemic stroke and massive pulmonary thromboembo-lism Komar M. MD, PhD, Prof. Podolec P. MD, PhD, Prof. Przewłocki T. MD, PhD, Stępniewski J. MD
Keywords: PFO, thrombophilia, ischemic stroke, pulmonary thromboembo-lism Background Patent foramen ovale (PFO) is a congenital cardiac lesion that frequently persists into adulthood. Although most patients with a PFO are asymptomatic, a variety of clinical manifestations may be associated with PFO, most importantly cryptogenic stroke. The prevalence of PFO is higher in patients with cryptogenic stroke, particularly those under age 55 years in whom PFO is more likely to play a causal role. Approximately 40 percent of ischemic strokes in adults …