(IV-1C.3a, IV-2A.O) 38-year old female patient with a congenitally corrected transposition of the great arteries Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Maria Olszowska, Piotr Podolec
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-1C.3a, V-2B.O ) 25 – year old patient with a transposition of the great arteries and arrhythmia Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Paweł Iwaszczuk, Maria Olszowska, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
Posted in – Others, 1. Abnormalities of the position and connection of the heart and vessels, 2. Arrhythmias secondary to rare structural diseases of the heart, 3. Great arteries, B. Due to congenital heart diseases, C. Veins and arteries, Case presentations, IV. Rare congenital cardiovascular diseases, V. Rare arrhythmias
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(IV-1C.3/II-2A.1) 41-year old patient with arterial pulmonary hypertension and unilateral pulmonary artery absence Blaszczak Piotr MD PhD, Grzywna Ryszard MD PhD, Gorczyca Daria MD, Siudak Łukasz MD
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
Posted in 1. Abnormalities of the position and connection of the heart and vessels, 1. Atresia of the pulmonary artery, 2. Inborn anomalies of the pulmonary vessels, 3. Great arteries, A. Anomalous morphology, C. Veins and arteries, Case presentations, II. Rare diseases of pulmonary circulation, IV. Rare congenital cardiovascular diseases
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(IV-1C.3a) Patient after operation of complex congenital heart disease with left ventricle ischaemia Agnieszka Żygadło MD, Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, PhD, Monika Smaś-Suska MD, Natalia Dłużniewska MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski, MD PhD, pediatric cardiac surgeon Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow COMMENT Computed tomography picture suggests that the homograft compresses the left coronary artery causing exercise ischemia. The homograft, in my opinion, should be replaced surgically. Coronary angiography should be performed, in order to investigate coronary arteries status. Reconsultation should be done before deciding for any coronary intervention coronary angiography. EXPERT: Tomasz Mroczek, MD PhD, pediatric cardiac surgeon …
(IV-1C.3.o) Patient with Taussig-Bing syndrome Drabik L., MD, Tomkiewicz-Pająk L., MD, PhD, Prof. Olszowska M., MD, PhD, Prof. Podolec P., MD, PhD
Background Taussig-Bing syndrome is a rare congenital heart malformation consisting of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect. Taussig-Bing syndrome is frequently associated with other cardiac abnormalities: right ventricular outflow tract obstruction, aortic arch obstruction and unusual coronary pattern [1].There are essential differences between Taussig-Bing syndrome and transposition of the great arteries with ventricular septal defect and overriding pulmonary artery. Taussig-Bing syndrome is characterized by true double-outlet right …
(IV-1C.3b) 21-year-old male with Truncus Arteriosus Type I Komar M. , Wilkołek P. , Kopeć G. , Sobień B. , Stępniewski J. , Tyrka A., Widlińska B., Podolec P.
Experts: Skalski J., Pająk J., Olszowska M., Tomkiewicz- Pająk L.
Background Truncus arteriosus communis (TAC) is a rare congenital heart disease appearing in 0.034 to 0.56 per 1,000 newborns and representing 1.4% to 2.8% of all cases of congenital heart diseases. In this anomaly, a single arterial trunk arises from the heart, overrides the interventricular septum, and supplies systemic, pulmonary, and coronary circulations. Without surgical treatment, 80% of patients die within the first year of life, usually in early infancy. Repair of TAC during the neonatal and early infant period …