(IV-2A.1) Patient with Tetralogy of Fallot after surgery with VSD, pulmonary hypertension and symptoms of heart failure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD. PhD, Prof. Maria Olszowska MD. PhD, Prof. Piotr Podolec MD, PhD.
Background Tetralogy of Fallot is a congenital cardiac malformation that consists of an interventricular communication, also known as a ventricular septal defect, obstruction of the right ventricular outflow tract, override of the ventricular septum by the aortic root, and right ventricular hypertrophy. Case presentation A 40-year-old woman after correction of tetralogy of Fallot (ToF) was admitted to hospital due to deterioration in exercise tolerance (NYHA functional class III). Surgical correction was performed at the age of 3 years. She was …
(IV-3B) 58-year-old patient with DILV after Waterstone procedure Katarzyna Mizia-Stec MD, PhD, Joanna Wieczorek, MD
Background Nowadays we can observe increasing number of grown-up congenital heart diseases, due to remarkable improvement in survival of pediatrics patients. Most of adult patients have undergone palliative operation in first years of life. Patients with univentricular heart present a multiple variety of malformations: missing or hypoplastic left or right ventricle, connected with corresponding valvular and great vessels anomalies. In such cases, most patients have restricted pulmonary blood flow, palliatively treated in childhood by surgically made systemic-to-pulmonary shunts. Examples of …
(IV-1B.1a) 55 years old patient with congenital heart malformation Joanna Stanisz-Kempa, Daniel Jakubowski, Maria Kasztelan- Masłowska, Barbara Monastyrska-Cup, Romuald Twardowski, Mariusz Skowerski, Zbigniew Gąsior
Background Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium(cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is subdivided by a thin membrane, resulting in three atrial chambers. Cor triatriatum is a rare congenital anomaly with a ratio of men to women of 1.5:1 [1] Cor triatriatum represents 0.1% -0,4% of all congenital cardiac malformations and usually refers to the left atrium. [2-3]In cor triatriatum sinister the left atrium is divided by a fibromuscular …
(IV-2A.1) Uncorrected Tetralogy of Fallot and Ischemic Heart Disease in a 57 Years Old Man prof.E.Ereminienė; prof. J. Vaškelytė; res.R.Ordienė; res.B.Kaminskaitė; res.T.Lapinskas; E.Kazakauskaitė
Background Tetralogy of Fallot (ToF), first described in 1888, comprises of an interventricular septal defect, right ventricular outflow tract obstruction, an overriding aorta, and right ventricular hypertrophy (RVH). It is the most common form of cyanotic congenital heart disease (10% of all cases). It is usually detected in early infancy due to symptoms related to cyanosis and right to left shunting of blood through a large ventricular septal defect. Uncorrected, it is associated with a very poor prognosis, with only …
(IV-2A.1) 43-year-old patient with unoperated Tetralogy of Fallot (ToF) lek. Agnieszka Sikora-Puz, dr n.med. Maciej Haberka, dr n.med. Leszek Szymański, lek. Piotr Pysz, prof. dr hab. n. med. Zbigniew Gąsior
Background Tetralogy of Fallot is a congenital cyanotic heart defect composed of four characteristics: large ventricular septal defect (VSD) – malaligment type, overriding aorta, right ventricular hypertrophy and right ventricular outflow obstruction. The location of the obstruction can be anywhere along the right ventricular outflow-infundibulum, pulmonic valve, the annulus of the pulmonic valve, the main pulmonary arteria (PA), or in the branch or peripheral pulmonary arteries. The degree of obstruction in the right ventricle outflow truck can range mild to …
(IV-1D.1o) 47-year-old patient with severe tricuspid regurgitation Sarnecka A. MD, Kopeć G. MD, PhD, Leśniak-Sobelga A. MD, PhD, Prof. Podolec P. MD, PhD
Background Pathological tricuspid regurgitation is more often secondary than due to a primary valve lesion. Isolated primary tricuspid regurgitation progresses slowly and can be well-tolerated for years. However, the data on the natural history of this heart disease suggest that the prognosis is poor. The timing of surgical treatment of severe isolated tricuspid regurgitation can be difficult. The valve repair is preferable method of surgery. Case presentation Presentation A 47-year-old man with severe tricuspid regurgitation and suspicion of Ebstein anomaly …
(IV-5A.2) Adult patient with common artery truncus and RV-PA conduit stenosis Lidia Tomkiewicz-Pająk MD, PhD , Prof. Maria Olszowska MD, PhD, Monika Komar MD, PhD, Prof. Piotr Podolec MD, PhD Grzegorz Kopeć MD, PhD, Jakub Podolec MD.
Background Truncus arteriosus communis (TAC) is a rare congenital heart disease appearing in 0.034 to 0.56 per 1,000 newborns and representing 1.4% to 2.8% of all cases of congenital heart disease . In this anomaly, a single arterial trunk arises from the heart, overrides the interventricular septum, and supplies systemic, pulmonary, and coronary circulations. Without surgical treatment, 80% of patients die within the first year of life, usually in early infancy. Repair of TAC during the neonatal and early infant …
(IV-5A.2) Adult patient with endocarditis after the Ross-Konno procedure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, Maria Olszowska MD, PhD, Grzegorz Kopeć MD, PhD
Background The Ross procedure is a type of valve surgery where the patient’s pulmonary valve is removed and switched to the aortic position. In the pulmonary position , a homograft is placed. The Konno modification of the Ross procedure allows an autograft aortic valve replacement in children with annular and subannular hypoplasia. The Ross-Konno procedure enables potential for growth of the pulmonary autograft in the aortic position. The lifelong anticoagulation can be avoided [1,2]. Meta-analysis of thirty-nine studies (n=5031) shows …
(IV-1D.2c) 20-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.
Background Aortic stenosis (AS) is the most common valvular heart disorder. The prevalence increases with age and is estimated on 2-7% in population over 65 years old. Congenital AS is often associated with bicuspid aortic valve. Deterioration of the left ventricle (LV) systolic function is a predictor of the worse outcome after aortic valve replacement (AVR). Among the asymptomatic patients with preserved LV systolic function the risk of death is relatively low- about 1%, but increases significantly when symptoms occur. …
(IV-1D.2c) 17-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.
Background Bicuspid aortic valve (BAV) is the most common heart defect that occurs in 1-2% live births. BAV is associated with abnormalities of elastic fibres in aortic media that often leads to aortic dilatation. Moreover, aortic stenosis (AS) may develop, even at a young age. Patients with AS can remain asymptomatic for many years. Among the asymptomatic patients with preserved LV systolic function the risk of death is about 1%, but increases significantly when symptoms occur. Deterioration of the left …