(IV-1D.2c) 20-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.

Background Aortic stenosis (AS) is the most common valvular heart disorder. The prevalence increases with age and is estimated on 2-7% in population over 65 years old. Congenital AS is often associated with bicuspid aortic valve. Deterioration of the left ventricle (LV) systolic function is a predictor of the worse outcome after aortic valve replacement (AVR). Among the asymptomatic patients with preserved LV systolic function the risk of death is relatively low- about 1%, but increases significantly when symptoms occur. …

Posted in 1. Abnormalities of the position and connection of the heart and vessels, 2. Left heart valves, D. Valves, default, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-1D.2c) 17-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.

Background Bicuspid aortic valve (BAV) is the most common heart defect that occurs in 1-2% live births. BAV is associated with abnormalities of elastic fibres in aortic media that often leads to aortic dilatation. Moreover, aortic stenosis (AS) may develop, even at a young age. Patients with AS can remain asymptomatic for many years. Among the asymptomatic patients with preserved LV systolic function the risk of death is about 1%, but increases significantly when symptoms occur. Deterioration of the left …

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The next CRCD tele-conference meeting

Next tele-conference meeting will take place on the 25-th of February 2013. For all interested in submitting difficult, rare cases please contact us on Facebook or rarediseases@szpitaljp2.krakow.pl

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(II-1A.5) 27- year old male with pulmonary hypertension and pate Andris Skride, MD

Expert’s conclusions: The patient should undergo pulmonary thromboendarterectomy. Authors: Andris Skride, MD1 1 Pauls Stradins Clinical University Hospital Latvian Cardiology Center   case presentations and videos are provided for private use only

Posted in 1. Pulmonary hypertension, 5. Chronic thromboembolic pulmonary hypertension, A. Low-prevalence pulmonary hypertension, Case presentations, default, II. Rare diseases of pulmonary circulation | Leave a comment

Programme of Ist International Conference on Rare Cardiovascular Diseases

I International Conference on Rare Cardiovascular Diseases 18 – 19 October 2012, Krakow, Poland Venue: John Paul II Hospital in Krakow Organizer: Centre for Rare Cardiovascular Diseases in John Paul II Hospital in Krakow DAY 1 THURSDAY, 18 October 2012 15.30-17.00 Session I (in Polish) Choroby rzadkie układu krążenia w Polsce Rare cardiovascular Diseases in Poland Prowadzenie (Moderators): Tomasz Grodzicki, Piotr Podolec Wystąpienia (Addresses): Krzysztof Chlebus – Podsekretarz Stanu w Ministerstwie Zdrowia Marek Sowa – Marszałek Województwa Małopolskiego Jerzy Sadowski …

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