(IV-2A.1) Uncorrected Tetralogy of Fallot and Ischemic Heart Disease in a 57 Years Old Man prof.E.Ereminienė; prof. J. Vaškelytė; res.R.Ordienė; res.B.Kaminskaitė; res.T.Lapinskas; E.Kazakauskaitė

Background Tetralogy of Fallot (ToF), first described in 1888, comprises of an interventricular septal defect, right ventricular outflow tract obstruction, an overriding aorta, and right ventricular hypertrophy (RVH). It is the most common form of cyanotic congenital heart disease (10% of all cases). It is usually detected in early infancy due to symptoms related to cyanosis and right to left shunting of blood through a large ventricular septal defect. Uncorrected, it is associated with a very poor prognosis, with only …

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(IV-2A.1) 43-year-old patient with unoperated Tetralogy of Fallot (ToF) lek. Agnieszka Sikora-Puz, dr n.med. Maciej Haberka, dr n.med. Leszek Szymański, lek. Piotr Pysz, prof. dr hab. n. med. Zbigniew Gąsior

Background Tetralogy of Fallot is a congenital cyanotic heart defect composed of four characteristics: large ventricular septal defect (VSD) – malaligment type, overriding aorta, right ventricular hypertrophy and right ventricular outflow obstruction. The location of the obstruction can be anywhere along the right ventricular outflow-infundibulum, pulmonic valve, the annulus of the pulmonic valve, the main pulmonary arteria (PA), or in the branch or peripheral pulmonary arteries. The degree of obstruction in the right ventricle outflow truck can range mild to …

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(IV-2A.1) Adult patients with Fallot Syndrom Lidia Tomkiewicz- Pajak MD., PhD., Joanna Luszczak MD., Prof. Piotr Podolec MD., PhD.

Background Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart disease. It is caused by the antero-supetior displacement of the infundibular septum what leads to the onset of the components of the ToF: malaligned ventricular septal defect (VSD), overriding aorta, right ventricular outflow tract obstruction (RVOTO) and, secondary, right ventricle (RV) hypertrophy. Uncorrected ToF has short life expectancy- about 25% of patients survive to age of 10 years and only 5% to age of 40 years[1,2]. However, long-term …

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(IV-2A.3) Ventricular septal defect and pulmonary atresia Agnieszka Sarnecka MD, Grzegorz Kopeć MD. PhD, Prof. Piotr Podolec MD. PhD

Background Pulmonary atresia with ventricular septal defect (PA + VSD) is a cyanotic congenital heart disease, also called Tetralogy of Fallot with pulmonary atresia. The intracardiac anatomy is similar to tetralogy but there is no direct communication between the right ventricle and pulmonary arteries. Major problems with surgical treatment are related to complexity of the pulmonary vascular bed that may make repair impossible. Case presentation We present a case of a 50-year old woman with congenital heart disease who was …

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(IV-2A.1) 56 -year-old male with Tetralogy of Fallot Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, Maria Olszowska MD, PhD, Prof. Piotr Podolec Md, PhD

Background Tetralogy of Fallot (ToF) is the most common cyanotic congenital heart disease. It is caused by the antero-superior displacement of the infundibular septum what leads to the onset of the components of the ToF: malaligned ventricular septal defect (VSD), overriding aorta, right ventricular outflow tract obstruction (RVOTO) and, secondary, right ventricle (RV) hypertrophy. Uncorrected ToF has short life expectancy- about 25% of patients survive to age of 10 years and only 5% to age of 40 years[1,2]. However, long-term …

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(IV-2A.1) 18-year-old patient with tetralogy of Fallot and coronary artery abnormality Smaś-Suska M.MD, Tomkiewicz-Pająk L. MD,PhD, Tyrka A. MD, Olszowska M. MD, PhD, Miszalski-Jamka T. MD, PhD, Podolec J. MD

Keywords: coronary artery abnormality, tetralogy of Fallot Background Tetralogy of Fallot is one of the most common cyanotic congenital cardiac diseases. This heart defect consists of ventricular septal defect, obstruction of the right ventricular outflow tract, overriding aorta and right ventricular hypertrophy. About 3% of patients have anomalous left anterior descending coronary artery which may necessitate a conduit type of repair. Conduits connect right ventricle and main pulmonary artery. There are two types of conduits: valved and non-valved. About 40% …

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