(II-1.A.4d) 30-year-old patient with arterial pulmonary hypertension and ascending aortic aneurysm Natasza Herman, Paweł Prochownik, Urszula Gancarczyk, Monika Komar, Bartosz Sobień, Piotr Podolec

  EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

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(II-1A.4d) 71-year-old patient with patent ductus arteriosus P. Prochownik, A. Sarnecka MD, G. Kopeć MD, PhD, M. Komar MD, PhD, Prof. P. Podolec MD, PhD

  BRIEF COMMENTS EXPERT: Krzysztof Szymoński, MD Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland COMMENT Due to current ESC guidelines the patient qualifies for PDA closure. Tricuspid valvuloplasty may also be considered. EXPERT: Grzegorz Kopeć, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow COMMENT Because there is no possibility of pulmonary hypertension targeted treatment the patient qualifies for PDA closure. Coexisting tricuspid regurgitation seems to be secondary to …

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(II-1A.4b) Pulmonary arterial hypertension associated with HIV and HCV infection Michał Furdal, Ewa Mroczek, Jakub Stępniewski

Background Pulmonary arterial hypertension (PAH) is a rare, but one of the most frequent complications of HIV infection. 3- year survival of patients with HIV related PAH (HIV-PAH) remaining in functional class III or IV by WHO (FC WHO) reaches approximately 20-30%. It is believed that highly active antiretroviral therapy (cART) or dysfunction of immune system and CD4 lymphocytes has less likely influence on the occurrence or the course of PAH. There is still limited data on the utilization of …

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(II-1A.4d) 47 years old female with Patent Ductus Arteriosus and Pulmonary Hypertension. Jakub Stępniewski MD, Grzegorz Kopeć MD, PhD, Hanna Dziedzic-Oleksy MD, Anna Tyrka MD, Prof. Piotr Podolec MD, PhD

Background Ductus arteriosus (DA) is a vascular connection between the main pulmonary artery and the aorta that allows blood to bypass the fetus’s non-functioning lungs. After delivery, the DA undergoes active constriction and obliteration eventually. A patent ductus arteriosus (PDA) occurs when the DA fails to close postnatally. PDA is an uncommon clinical finding in adult population. Improvement of survival of premature infants at risk for PDA and an increase in cases discovered incidentally, the incidence of PDA is rising …

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(II-1A.4d) Patient with ventricular septal defect and Eisenmenger syndrome with gynecological complications Magdalena Kaźnica-Wiatr MD, Magdalena Nowacka MD, Grzegorz Kopeć MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

Background Eisenmenger syndrome is defined as pulmonary vascular obstructive disease which develops as a consequence of preexisting large left-to-right shunt such that pulmonary artery pressures approach systemic values and the direction of the flow becomes bidirectional or right-to-left. Congenital heart defects that can lead to Eisenmenger syndrome include “simple” defects like ASD, VSD, PDA or “complex” like AVSD, truncus arteriosus, aortopulmonary window and univentricular heart. Elevated pulmonary vascular resistance usually occurs in infancy, by the age of 2 years. Clinical …

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(II-1A.4d) 62-year-old female with Ostium Secundum Atrial Septal Defect (ASD t. II) and coexisting pulmonary hypertension Stepniewski J., Podolec M., Komar M., Wójtowicz M., Tyrka A., Nowacka M., Kopeć G., Rubiś P., Tomkiewicz-Pająk L.,
Experts: Sadowski J., Kapelak B., Podolec P.

Background Ostium Secundum Atrial Septal Defect (ASD II) is the most commonly diagnosed type of ASDs. It accounts for about 75% of all ASD cases, representing approximately 7% of all congenital cardiac defects and 30-40% of all congenital heart disease in patients older than 40 years. It is characterized by a defect in the interatrial septum allowing pulmonary venous return to pass directly from the left atrium to the right atrium. The condition can be left undiagnosed for many years …

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