(IV-3.B) Long-term survival in unoperated double-inlet ventricle M. Haberka, M. Biedroń, E. Jastrzębska-Maj, L. Szymański, K. Bańska, M. Skowerski, Z. Gąsior



EXPERT: Prof. Henryk Siniawski MD, PhD, cardiac surgeon
Affiliation: German Heart Instiute, Berlin, Germany
I would recommend RHC in order to exclude pulmonary hypertension. Optimal medical treatment is necessary to protect the patient form cardiac decompensation in the future.

EXPERT: Assoc. Prof. Jacek Pająk, MD, PhD, pediatric cardiac surgeon
Affiliation: Silesian Center for Heart Diseases, Zabrze, Poland
It appears that conservative treatment and watchful observation would be the most reasonable proceeding.

EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD, pediatric cardiac surgeon
Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland
Circulatory system is well balanced at the moment. It is important to rule out pulmonary hypertension. In case of progressive circulatory deterioration HTx should be considered

EXPERT: Prof. Bogusław Kapelak MD, PhD, cardiac surgeon
Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland
The patient is currently not feasible for surgical treatment. In the future HTx or heart and lung transplantation may be required in case of advanced heart failure


1. Right heart catheterization is recommended in order to definitely exclude pulmonary artery hypertension.
2. Conservative treatment with close follow-up seems the best option at present.


“Development of the European Network in Orphan Cardiovascular Diseases”
“Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

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