(IV – 2A.1; IV – 5A.2) Patient with congenital heart desease – Tetralogy of Fallot – after surgical correction and with severe pulmonic valve regurgitation and moderate tricuspid valve regurgitation
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5A) 42-year-old patient with aortic aneurysm, after correction of VSD, PDA and narrowing of pulmonary trunk Justyna Błaut-Jurkowska MD, Lidia Tomkiewicz-Pająk MD, PhD, Prof. Maria Olszowska MD, PhD, Klaudia Knap MD, Joanna Łuszczak MD, Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5.A2) An 18-year-old patient after baloon aortic valvuloplasty with severe aortic regurgitation and pulmonary hypertension Paweł Prochownik, Monika Komar, Bartosz Sobień, Urszula Gancarczyk, Natasza Herman, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-6) 52 year old patient with aneurysm of ascending aorta, composite aortic valve disease and persitent ductus arteriosus Botalli Lidia Tomkiewicz – Pająk MD; Natalia Dłużniewska MD; Justyna Błaut – Jurkowska MD; Paweł Iwaszczuk MD; prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV – 2A.1) Patient after operation of tetralogy of Falot with patent blalock – Taussig Natalia Dłużniewska MD; dr n. med. Lidia Tomkiewicz – Pająk MD, Jakub Stępniewski; PhD; prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV- 2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Piotr Podolec Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT Despite the lack of symptoms there is a significant leakage, reduced contractility of the left and right ventricle and the pulmonary artery trunk extension. It seems reasonable to close of atrial septal defect – to consider is the choice of method (percutaneous using Amplatz device or surgical, which additional advantage is a possibility of leaving a little septal communication …
(IV-2A.1) Patient after corection of Tetralogy of Fallot with pulmonary valve regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Krzysztof Szymoński, MD Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow, Poland COMMENT Regarding whole clinical presentation biological pulmonary valve replacement and tricuspid valvuloplasty seems appropriate, especially taking into account that the patient is planning pregnancy. Concomitant right ventricular plasty may also be considered. CONCLUSIONS Regarding the patient is planning pregnancy, biological pulmonary valve replacement together with tricuspid valvuloplasty seems reasonable, concomitant right ventricular plasty may also be considered. “Development of the …
(IV-5B.1 ) Patient with congenital heart disease – TGA, hypoplasia of right ventricle, left atrioventricular valve atresia and VSD Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Grzegorz Kopeć, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT There are no sufficient evidence from clinical trials for the use of sildenafil in presented case. EXPERT: Lidia Tomkiewicz-Pająk, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT In current literature there are no data for beneficial influence of sildenafil in presented clinical situation. CONCLUSIONS 1. Psychological care indicated. 2. Cardiostimulator …
(IV-2A.1 ) Adult patient with Tetralogy of Fallot after Blalock-Taussing anastomosis Agnieszka Żygadło MD, Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, PhD, Monika Smaś-Suska MD, Natalia Dłużniewska MD, Joanna Łuszczak MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski, MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT There are indications for surgical intervention. However, heart catheterisation should be performed in the first place. Optimal management would be VSD and shunt closure, and creating communication between atria. Minimal ventriculotomy may also be considered. EXPERT: Prof. Zbigniew Kordon, MD, PhD Affiliation: Department of Pediatric Cardiology, Jagiellonian University Medical College, Krakow, Poland COMMENT Pulmonary hypertension is suspected in …