BRIEF COMMENTS
EXPERT: Lidia Tomkiewicz-Pająk MD, PhD
Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow
COMMENT
In my opinion Fontan procedure wouldn’t be suitable for this patient. There is a significant tricuspid regurgitation, function of single ventricle wouldn’t be sufficient after Fontan operation. The best option is heart transplantation.
EXPERT: Prof. Lesław Szydłowski MD, PhD
Affiliation: 1st Department of Paediatric Cardiology, Medical University of Silesia, Katowice-Ligota, Poland
COMMENT
In case of significant tricuspid regurgitation Fontan operation is charged with high risk of unsuccessful course. If pulmonary resistance is low, Glenn procedure would be an option but there will be a risk of pulmonary hypertension development
EXPERT: Assoc. Prof. Bogusław Kapelak MD
Affiliation: Department of Cardiovascular Surgery and Transplantology, John Paul II Hospital, Krakow
COMMENT
Heart transplantation would be the best option. At this point it seems quite safe. Additional procedures may increase pulmonary resistance and ruin patient’s chances for transplantation.
CONCLUSIONS
1) Probably Glenn procedure will improve blood oxygenation. Close observation after surgery is required.
2) Consider heart transplantation as the treatment of choice.
“Development of the European Network in Orphan Cardiovascular Diseases”
„Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
