(IV-1C.1) 60-year-old patient with total anomalous pulmonary venous return and atrial septal defect Sarnecka A. MD, Kopeć G. MD, PhD, Tomaszewski M. MD, PhD, Prof. Podolec P. MD, PhD
Experts: Prof. Roland Hetzer, PhD; Jacek Kołcz, MD, PhD; Lidia Tomkiewicz-Pająk, MD, PhD; Zbigniew Kordon, MD, PhD; Prof. Egle Ereminiene, MD, PhD

 

BRIEF COMMENTS

EXPERT: Prof. Roland Hetzer, MD PhD, cardiac surgeon

Affiliation: Deutsches Herzzentrum, Berlin, Germany

COMMENT

Unusual case – usually such patients are operated short after birth. There are a few aspects to consider: 6 minutes walking test result was reduced, but not very low. Future problem will be tricuspid regurgitation. Another aspect is whether complete or partial correction should be performed. If patient wants operation, it should be considered. Risk of the surgical correction is about 5-10%. There is no indication for anticoagulants if the only problem is congenital heart disease.

 

EXPERT: Dr Jacek Kolcz, MD PhD, pediatric cardiac surgeon

Affiliation: Department of Pediatric Cardiac Surgery, University Children’s Hospital of Krakow, Poland

COMMENT

There is no fixed pulmonary hypertension, no pulmonary or tricuspid regurgitation. The patient should be considered a candidate for surgery.

 

EXPERT: Dr Lidia Tomkiewicz-Pająk, MD PhD, cardiologist

Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland

COMMENT

Right ventricle function should be carefully evaluated. If it is poor, the result of the surgery will be unfavorable .

 

EXPERT: Dr Zbigniew Kordon MD, PhD, pediatric cardiologist

Affiliation: Department of Pediatric Cardiology, University

Children’s Hospital of Krakow, Poland

COMMENT

RV is overloaded, Qp/Qs is approximately 4:1. From the surgical point of view, performing a procedure is not very complicated. But question is what happed when we diminish the RV overload. In my opinion, we should correct but not completely close ASD.

 

CONCLUSION

Decision regarding the surgical approach should be discussed with the patient thoroughly. It is her decision. Modification of the antiarrhythmic treatment (propafenon 3x/day) should be considered.

Anticoagulants are not indicated for this patient.

 


“Development of the European Network in Orphan Cardiovascular Diseases”
„Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”

This entry was posted in 1. Abnormalities of the position and connection of the heart and vessels, 1. Systemic veins, C. Veins and arteries, Case presentations, IV. Rare congenital cardiovascular diseases. Bookmark the permalink.

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