(II-1C.1) 23-year-old man with Down syndrome, complete AV canal, Eisenmenger syndrome, and elevated Pulmonary Capillary Wedge Pressure (PCWP) Kopeć G., Stępniewski J., Tyrka A.,

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Keywords: Eisenmenger syndrome, Pulmonary Capillary Wedge Pressure, Down syndrome Background Pulmonary hypertension (PH) is a hemodynamic and pathophysiological condition defined as an increase in mean pulmonary arterial pressure (PAP)≥ 25 mmHg at rest as assessed by right heart catheterization. PH can be found in multiple clinical conditions. Complete atrioventricular canal (CAVC), an uncommon CHD often associated with Down syndrome, is characterised by an ostium primum atrial septal defect, a common atrioventricular valve and a variable deficiency of the ventricular septum …

Posted in 1. Pulmonary hypertension, 1. Pulmonary hypertension in a patient with congenital shunt and left ventricular dysfunction, C. Overlap pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation | Leave a comment

(II-1C.2) Patient with atrial septal defect pulmonary embolism and pulmonary hypertension Podolec M., Kopeć G., Tytka A.
Experts: Lang I.

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Posted in 1. Pulmonary hypertension, 2. Pulmonary hypertension associated with congenital heart disease complicated by thromboembolic disease, C. Overlap pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation | Leave a comment

(II-1C.O) 54-year old male with severe kyphoscoliosis and pulmonary hypertension Sobień B., Kopeć G., Rubiś P., Tomkiewicz Pająk L., Barczyk K., Podolec P.
Experts: Prokop-Staszecka A., Kłosiński P., Fijałkowska A., Bederski K., Podolec P.

Background A 54-year-old caucasian male was admitted to our clinic with symptoms of cardiac and pulmonary failure. The patient suffered from inherited severe kyphoscoliosis of unknown etiology. At the time of admission he was compensated, in NYHA functional class III. Exercise dyspnea and a drop in effort tolerance were main complaints. Case presentation The patient was admitted to our clinic in May 2011due to clinical worsening of cardiopulmonary insufficiency. On admission he was in NYHA functional class III. No peripheral …

Posted in 1. Pulmonary hypertension, C. Overlap pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation, Others | Leave a comment