(I-1C.O) 57-year-old patient with a coronary arteries anomaly Monika Smaś-Suska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Piotr Musiałek MD, PhD, Natalia Dłużniewska MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(I-1C.4) Overlap cardiomyopathy – coexistence of hypertrophic and restrictive cardiomyopathy phenotypes in one patient Sylwia Wiśniowska-Śmałek MD, Paweł Rubiś MD, PhD, Monika Dzieciuch- Rojek, Dawid Kudliński MD, Agata Leśniak-Sobelga MD, PhD, Magdalena Kostkiewicz MD, PhD Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Roland Hetzer, MD, PhD Affiliation: German Heart Instiute, Berlin, Germany COMMENT Considering clinical data and results of the medical tests the patient is likely a future heart transplantation candidate. No relevant ventricular arrhythmias were detected and I would not recommend ICD implantation. However due to coexistent scoliosis the patient should undergo lung function tests and pulmonological consultation to plan the best possible post-op management. The scoliosis itself is not a contraindication to HTx. EXPERT: Assoc. …
(II-1C.O) What is the coincidence of pulmonary arterial hypertension associated with congenital cardiac shunt and hypertrophic cardiomyopathy in patient with trisomy 21 Wojciech Wróbel MD, PhD, Prof.Katarzyna Mizia-Stec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow COMMENT Diagnosis of cardiomyopathy needs closer evaluation. Ventricular hypertrophy and pulmonary arterial hypertension might be consequences of congenital heart defect, not necessarily cardiomyopathy. It is not clear why the patient wasn’t operated in the past? EXPERT: Prof. Katarzyna Mizia-Stec MD, PhD Affiliation: 1st Department of Cardiology, Medical University of Silesia, Katowice,Poland COMMENT Ventricle hypertrophy was first noticed in 2005. Question …
(I-1C.4) 44-year-old patient with anomalous circumflex artery shunt to the right atrium and moderate mitral regurgitation Podolec J. MD PhD, Nosal M. MD, Górkiewicz-Kot I. MD PhD, Sobczyk D. MD PhD, Kopec G. MD, PhD, prof. Sadowski J. MD, PhD, prof. Zmudka K. MD, PhD
BRIEF COMMENTS EXPERT: Prof. Henryk Siniawski MD, PhD Affiliation: Deutsches Herzzentrum, Berlin, Germany COMMENT Surgery seems essential – it’s young patient with large ischemic area and LV dilatation. He has limited quality of life. Perhaps microreconstruction might be feasible. In case of patients disagreement for surgical treatment, I suggest exercise test 3 times a year – positive test with chest pain may motivate patient to agree for the operation.. Mitral regurgitation may have ischemic origin and may progress very …
(I-1C.O) 28 -year – old man with anomalous origin of the right coronary artery from the ascending aorta. Sylwia Wiśniowka-Śmiałek MD, Agata Leśniak-Sobelga MD, Paweł Rubiś MD, Ph.D, Maciej Krupiński MD.
Background Coronary artery anomalies (CAAs) are a diverse group of congenital malformations, which clinical manifestations and pathology are highly variable . Being rare, they are recognized cause of myocardial ischemia and occasionally sudden cardiac death . The frequency of anomalous aortic origin of the coronary arteries is noted in 0,6 to 1,2 % of patients (based on coronary angiography), with significant higher incidence in young victims of sudden cardiac death in comparison to adults (4-15% versus 1% respectively). There is …
(I-1C.4) Patient with coronaro-pulmonary fistula Justyna Błaut-Jurkowska MD, Leszek Drabik MD, Piotr Musiałek MD, PhD Lidia Tomkiewicz-Pająk MD, PhD, Bartosz Laskowicz MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Prof. Tadeusz Przewłocki MD, PhD
Background Coronary artery anomalies affect about 1% of the general population. The definition of the abnormal versus the normal coronary anatomy presents a complex problem. Defect may affect number of ostia, proximal course or termination. Many coronary anomalies don’t cause symptoms and remain undetected. However, they can be associated with chest pain, sudden death, cardiomyopathy, arrythmias and myocardial infarction. Case presentation We report a case of a 61-year-old Caucasian man referred to our Clinic. He had a history of coronary …