(IV-5A.2) Patient with stenotic conduit after surgical correction of Tetralogy of Fallot Dawid Kudliński MD, Magdalena Kostkiewicz MD, PhD, Agata Leśniak-Sobelga MD, Lidia Tomkiewicz-Pająk MD, PhD, Tomasz Miszalski-Jamka MD, PhD, Prof. Piotr Podolec MD, PhD

Background Tetralogy of Fallot is a one of congenital heart defects involving four anatomical abnormalities: pulmonary stenosis or pulmonary atresia, overriding aorta, ventricular septal defect, right ventricular hypertrophy. It is the most common cyanotic heart defect. The main symptoms are a bluish coloration of the skin caused by blood low in oxygen (cyanosis), a heart murmur and clabbing of fingers. Tetralogy of Fallot with atresia of the left pulmonary artery is presented by 10% of patients. Case presentation We present …

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(IV-5A.2) Patient with significant pulmonary valve regurgitation after Fallot operation Lidia Tomkiewicz-Pająk MD. PhD., Maria Olszowska MD. PhD., Prof. Piotr Podolec MD. PhD.

Background Tetralogy of Fallot (ToF) is the cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently present complications. They include: severe pulmonary regurgitation, right ventricular outflow tract obstruction, right ventricular dilation and dysfunction, residual …

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(IV-5B.1) Patient after Fontan operation Mroczek E. MD, PhD, Podolec J. MD, Kusa J. MD, PhD

Keywords: Fontan operation Background Tricuspid atresia accounts for about 0.7% of all congenital heart diseases. The tricuspid valve is absent, and there is no anatomic connection and direct communication between the right atrium and the right ventricle. Case description This 27-year-old female after Fontan operation is presented. The patient was born at term but was cyanotic. Diagnosis was made of tricuspid atresia with atrial septal defect (ASD) and ventricular septal defect (VSD). At age of 3.5 years a Fontan circulation …

Posted in 1. Fontan procedure, 5. Grown-up congenital cardiovascular diseases, B. After palliative procedures, Case presentations, IV. Rare congenital cardiovascular diseases | Leave a comment

(IV-5A.2) Patient after correction of Tetralogy of Fallot with pulmonary valve regurgitation and left pulmonary branch stenosis Tomkiewicz-Pająk L. MD, PhD, Podolec J. MD, Kopeć G. MD, PhD, Drabik L. MD, Assoc. Prof. Olszowska M. MD, PhD, Miszalski-Jamka T. MD, PhD, Assoc. Prof. Kostkiewicz M. MD, PhD, Tyrka A. MD

Keywords: correction of Tetralogy, pulmonary valve regurgitation, left pulmonary branch stenosis Background Tetralogy of Fallot (ToF) is a cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently develop complications such as severe pulmonary regurgitation, …

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(IV-5A.O) Adult patient after correction of tetralogy of Fallot with a single branch of the pulmonary artery Tomkiewicz-Pająk L., Drabik L., Krupiński M., Podolec J., Banyś P., Rubiś P., Podolec P.
Experts: Skalski J., Pająk J., Trojnarska O., Gąsior Z., Miszalski – Jamka T.

Background Tetralogy of Fallot is a rare congenital cardiac diseases occurring in one of every 35,0000-30,000 live births. This malformation consists of ventricular septal defect, obstruction of the right ventricular outflow tract, override of the ventricular septum by the aortic root, and in consequence right ventricular hypertrophy. It is the most common cyanotic heart defect. Abnormalities of the pulmonary arteries following palliative or corrective surgery for tetralogy of Fallot (TOF) are common. There are only a few written cases of …

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