(IV-5B.1) Heart failure in Fontan patient Lidia Tomkiewicz-Pająk, Monika Smaś –Suska, Maria Olszowska, Wojciech Płazak, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1) 31-year old patient after Fontan operation with systemic AV valve regurgitation Knap K. MD, Tomkiewicz- Pająk L. MD, PhD, Prof. Olszowska M. MD, PhD, Prof. Podolec P. MD, PhD, Smaś- Suska M. MD, Jurkowska- Błaut J. MD
EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV – 2A.1; IV – 5A.2) Patient with congenital heart desease – Tetralogy of Fallot – after surgical correction and with severe pulmonic valve regurgitation and moderate tricuspid valve regurgitation
“Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5A) 42-year-old patient with aortic aneurysm, after correction of VSD, PDA and narrowing of pulmonary trunk Justyna Błaut-Jurkowska MD, Lidia Tomkiewicz-Pająk MD, PhD, Prof. Maria Olszowska MD, PhD, Klaudia Knap MD, Joanna Łuszczak MD, Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5.A2) An 18-year-old patient after baloon aortic valvuloplasty with severe aortic regurgitation and pulmonary hypertension Paweł Prochownik, Monika Komar, Bartosz Sobień, Urszula Gancarczyk, Natasza Herman, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1 ) Patient with congenital heart disease – TGA, hypoplasia of right ventricle, left atrioventricular valve atresia and VSD Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Grzegorz Kopeć, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT There are no sufficient evidence from clinical trials for the use of sildenafil in presented case. EXPERT: Lidia Tomkiewicz-Pająk, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT In current literature there are no data for beneficial influence of sildenafil in presented clinical situation. CONCLUSIONS 1. Psychological care indicated. 2. Cardiostimulator …
(IV-5A.O) Patient with coarctation of the aorta and Tetralogy of Fallot with significant pulmonary valve regurgitation Lidia Tomkiewicz-Pająk MD, PhD, Tomasz Pawelec MD, PhD, Natalia Dłużniewska MD, Grzegorz Kopeć MD, PhD, Paweł Rubiś MD, PhD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Children’s Hospital, Krakow, Poland COMMENT Coexistence of Tetralogy of Fallot and coarctation of aorta is embriologically doubtful. Iatrogenic origin of the CoA should be taken under consideration. It might have also been a combination of VSD with pulmonary valve stenosis and coarctation of aorta as the primary defect. CONCLUSIONS 1) Percutaneous repair of pulmonary regurgitation should be taken under consideration EXPERTISE 1 …
(IV-5A.O)Patient after corection of Tetralogy of Fallot syndrome with aortic regurgitation Natalia Dłużniewska MD, Lidia Tomkiewicz-Pająk MD PhD, Prof Maria Olszowska MD, PhD, Prof Piotr Podolec MD PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski, MD PhD, cardiac surgeon Affiliation: Department of Pediatric Cardiac Surgery, University Children’s Hospital of Krakow, Poland COMMENT Mitral regurgitation appears to be the most problematic issue in this case. Is the mitral valve replacement really essential? Echocardiography shows moderate mitral regurgitation, probably conservative treatment is indicated with regular check-ups. Observation if the defect does not worsens. Surgical procedure will be difficult in this patient. EXPERT: Dr Lidia Tomkiewicz-Pająk, MD PhD, cardiologist Affiliation: Department of …
(IV-5A.2) Adult patient with common artery truncus and RV-PA conduit stenosis Lidia Tomkiewicz-Pająk MD, PhD , Prof. Maria Olszowska MD, PhD, Monika Komar MD, PhD, Prof. Piotr Podolec MD, PhD Grzegorz Kopeć MD, PhD, Jakub Podolec MD.
Background Truncus arteriosus communis (TAC) is a rare congenital heart disease appearing in 0.034 to 0.56 per 1,000 newborns and representing 1.4% to 2.8% of all cases of congenital heart disease . In this anomaly, a single arterial trunk arises from the heart, overrides the interventricular septum, and supplies systemic, pulmonary, and coronary circulations. Without surgical treatment, 80% of patients die within the first year of life, usually in early infancy. Repair of TAC during the neonatal and early infant …
(IV-5A.2) Adult patient with endocarditis after the Ross-Konno procedure Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, Maria Olszowska MD, PhD, Grzegorz Kopeć MD, PhD
Background The Ross procedure is a type of valve surgery where the patient’s pulmonary valve is removed and switched to the aortic position. In the pulmonary position , a homograft is placed. The Konno modification of the Ross procedure allows an autograft aortic valve replacement in children with annular and subannular hypoplasia. The Ross-Konno procedure enables potential for growth of the pulmonary autograft in the aortic position. The lifelong anticoagulation can be avoided [1,2]. Meta-analysis of thirty-nine studies (n=5031) shows …