(IV-3.B) Long-term survival in unoperated double-inlet ventricle M. Haberka, M. Biedroń, E. Jastrzębska-Maj, L. Szymański, K. Bańska, M. Skowerski, Z. Gąsior
BRIEF COMMENTS EXPERT: Prof. Henryk Siniawski MD, PhD, cardiac surgeon Affiliation: German Heart Instiute, Berlin, Germany COMMENT I would recommend RHC in order to exclude pulmonary hypertension. Optimal medical treatment is necessary to protect the patient form cardiac decompensation in the future. EXPERT: Assoc. Prof. Jacek Pająk, MD, PhD, pediatric cardiac surgeon Affiliation: Silesian Center for Heart Diseases, Zabrze, Poland COMMENT It appears that conservative treatment and watchful observation would be the most reasonable proceeding. EXPERT: Assoc. Prof. Jacek …
(IV-3B) 58-year-old patient with DILV after Waterstone procedure Katarzyna Mizia-Stec MD, PhD, Joanna Wieczorek, MD
Background Nowadays we can observe increasing number of grown-up congenital heart diseases, due to remarkable improvement in survival of pediatrics patients. Most of adult patients have undergone palliative operation in first years of life. Patients with univentricular heart present a multiple variety of malformations: missing or hypoplastic left or right ventricle, connected with corresponding valvular and great vessels anomalies. In such cases, most patients have restricted pulmonary blood flow, palliatively treated in childhood by surgically made systemic-to-pulmonary shunts. Examples of …
(IV-3B) The patient with TGA, VSD, PS after Rastelli procedure Lidia Tomkiewicz-Pająk MD. PhD., Maria Olszowska MD. PhD., Prof. Piotr Podolec MD. PhD.
Background Transposition of the great vessels is a congenital cyanotic heart defect. The hallmark of transposition of the great arteries is ventriculoarterial discordance, in which the aorta arises from the morphologic right ventricle and the pulmonary artery arises from the morphologic left ventricle. The Rastelli operation is performed for the repair of d-transposition of the great vessels with ventricular septal defect and pulmonary stenosis. During the surgery right ventricular outflow truckt – pulmonary arteries conduit is implanted and VSD is …
(IV-3A) Adult- patient after Fontan procedure with heterotaxy syndrome, vena cava inferior – pulmonary artery tunnel narrowing Tomkiewicz-Pająk L., Miszalski-Jamka T., Krupiński M., Banyś P., Olszowska M., Podolec M., Drabik L., Podolec P.
Experts: Janusz Skalski J., Jacek Kołcz J., Trojnarska O., Kopeć G., Miszalski- Jamka T.
Background Heterotaxy syndrome is a rare defect that involves the heart and other organs. It is a disorder that results in certain organs forming on the opposite side of the body. The incidence of typical forms is 2,5/100 000 births. Heterotaxy coming from greek word “heteros” meaning different and “taxis” meaning arrangement. These malformations are always associated with additional cardiac lesions such as univentricular heart (UV). The Fontan operation was introduced in 1968 and has become the definitive treatment for …