(II-1A.4d) Patient with ventricular septal defect and Eisenmenger syndrome with gynecological complications Magdalena Kaźnica-Wiatr MD, Magdalena Nowacka MD, Grzegorz Kopeć MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD

Background Eisenmenger syndrome is defined as pulmonary vascular obstructive disease which develops as a consequence of preexisting large left-to-right shunt such that pulmonary artery pressures approach systemic values and the direction of the flow becomes bidirectional or right-to-left. Congenital heart defects that can lead to Eisenmenger syndrome include “simple” defects like ASD, VSD, PDA or “complex” like AVSD, truncus arteriosus, aortopulmonary window and univentricular heart. Elevated pulmonary vascular resistance usually occurs in infancy, by the age of 2 years. Clinical …

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(II-1A.5) Chronic thromboembolic pulmonary hypertension Skaidrius MiliauskasMD, PhD, Deimante Hoppenot MD, PhD

Background Chronic thromboembolic pulmonary hypertension (CTEPH) is a life-threatening condition in which organised thrombi obstruct the pulmonary vessels, causing increased pulmonary vascular resistance, progressive pulmonary hypertension (PH) and right heart failure. CTEPH is associated with considerable morbidity and mortalities. Even if more recent papers suggest that the prevalence of CTEPH is up to 3.8% in survivors of acute pulmonary embolism, most experts believe that the true incidence of CTEPH after acute pulmonary embolism is 0.5–2%. CTEPH can be found in …

Posted in 1. Pulmonary hypertension, 5. Chronic thromboembolic pulmonary hypertension, A. Low-prevalence pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation | Leave a comment

(VII- II-1A.4d) Pregnancy in a patient with Eisenmenger syndrome Ewa Mroczek

Authors: Ewa Mroczek1 1Cardiology department Regional Hospital in Wrocław Research and Development Centre   case presentations and videos are provided for private use only

Posted in 1. Pulmonary hypertension, A. Low-prevalence pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation, VII. II. rare diseases of pulmonary circulation, VII*. Cardiovascular diseases in pregnancy | Leave a comment

(II-1A.5) 27- year old male with pulmonary hypertension and pate Andris Skride, MD

Expert’s conclusions: The patient should undergo pulmonary thromboendarterectomy. Authors: Andris Skride, MD1 1 Pauls Stradins Clinical University Hospital Latvian Cardiology Center   case presentations and videos are provided for private use only

Posted in 1. Pulmonary hypertension, 5. Chronic thromboembolic pulmonary hypertension, A. Low-prevalence pulmonary hypertension, Case presentations, default, II. Rare diseases of pulmonary circulation | Leave a comment

(II-1C.1) 23-year-old man with Down syndrome, complete AV canal, Eisenmenger syndrome, and elevated Pulmonary Capillary Wedge Pressure (PCWP) Kopeć G., Stępniewski J., Tyrka A.,

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Keywords: Eisenmenger syndrome, Pulmonary Capillary Wedge Pressure, Down syndrome Background Pulmonary hypertension (PH) is a hemodynamic and pathophysiological condition defined as an increase in mean pulmonary arterial pressure (PAP)≥ 25 mmHg at rest as assessed by right heart catheterization. PH can be found in multiple clinical conditions. Complete atrioventricular canal (CAVC), an uncommon CHD often associated with Down syndrome, is characterised by an ostium primum atrial septal defect, a common atrioventricular valve and a variable deficiency of the ventricular septum …

Posted in 1. Pulmonary hypertension, 1. Pulmonary hypertension in a patient with congenital shunt and left ventricular dysfunction, C. Overlap pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation | Leave a comment

(II-1C.2) Patient with atrial septal defect pulmonary embolism and pulmonary hypertension Podolec M., Kopeć G., Tytka A.
Experts: Lang I.

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  case presentations and videos are provided for private use only

Posted in 1. Pulmonary hypertension, 2. Pulmonary hypertension associated with congenital heart disease complicated by thromboembolic disease, C. Overlap pulmonary hypertension, Case presentations, II. Rare diseases of pulmonary circulation | Leave a comment

(II-1A.4d) 62-year-old female with Ostium Secundum Atrial Septal Defect (ASD t. II) and coexisting pulmonary hypertension Stepniewski J., Podolec M., Komar M., Wójtowicz M., Tyrka A., Nowacka M., Kopeć G., Rubiś P., Tomkiewicz-Pająk L.,
Experts: Sadowski J., Kapelak B., Podolec P.

Background Ostium Secundum Atrial Septal Defect (ASD II) is the most commonly diagnosed type of ASDs. It accounts for about 75% of all ASD cases, representing approximately 7% of all congenital cardiac defects and 30-40% of all congenital heart disease in patients older than 40 years. It is characterized by a defect in the interatrial septum allowing pulmonary venous return to pass directly from the left atrium to the right atrium. The condition can be left undiagnosed for many years …

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(II-1C.O) 54-year old male with severe kyphoscoliosis and pulmonary hypertension Sobień B., Kopeć G., Rubiś P., Tomkiewicz Pająk L., Barczyk K., Podolec P.
Experts: Prokop-Staszecka A., Kłosiński P., Fijałkowska A., Bederski K., Podolec P.

Background A 54-year-old caucasian male was admitted to our clinic with symptoms of cardiac and pulmonary failure. The patient suffered from inherited severe kyphoscoliosis of unknown etiology. At the time of admission he was compensated, in NYHA functional class III. Exercise dyspnea and a drop in effort tolerance were main complaints. Case presentation The patient was admitted to our clinic in May 2011due to clinical worsening of cardiopulmonary insufficiency. On admission he was in NYHA functional class III. No peripheral …

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