(IV-1D.2d) 21-year old patient with bicuspid aortic valve Monika Smaś-Suska, Lidia Tomkiewicz-Pająk, Natalia Dłużniewska, Maria Olszowska, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
( I – 2A.0; IV – 1D.2d ) Patient with artificial aortic valve with aneurysm of ascending aorta Natalia Dłużniewska MD; Lidia Tomkiewicz – Pająk MD, PhD; Aleksandra Lenart MD, Monika Smaś – Suska MD, Prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD, pediatric cardiac surgeon Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT Ascending aorta’s diameter has shown widening tendency. It is difficult to determine if the implanted AV is still suitable for the patient. I recommend consideration of AVR procedure (for example implantation of biological valve and plasty of the ascending aorta). Bioprothesis might improve the patient’s quality of life. Aortic homograft implantation would make possible …
Posted in 1. Abnormalities of the position and connection of the heart and vessels, 2. Connective tissue disorders causing aneurysmal disease, 2. Left heart valves, A. Aneurysmal disease of the aorta, Case presentations, D. Valves, I. Rare diseases of systemic circulation, IV. Rare congenital cardiovascular diseases, Others
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(IV-1D.2c) 20-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.
Background Aortic stenosis (AS) is the most common valvular heart disorder. The prevalence increases with age and is estimated on 2-7% in population over 65 years old. Congenital AS is often associated with bicuspid aortic valve. Deterioration of the left ventricle (LV) systolic function is a predictor of the worse outcome after aortic valve replacement (AVR). Among the asymptomatic patients with preserved LV systolic function the risk of death is relatively low- about 1%, but increases significantly when symptoms occur. …
(IV-1D.2c) 17-year-old male with asymptomatic aortic stenosis Joanna Łuszczak MD, Lidia Tomkiewicz- Pajak MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Paweł Rubiś MD, PhD, Jakub Podolec MD.
Background Bicuspid aortic valve (BAV) is the most common heart defect that occurs in 1-2% live births. BAV is associated with abnormalities of elastic fibres in aortic media that often leads to aortic dilatation. Moreover, aortic stenosis (AS) may develop, even at a young age. Patients with AS can remain asymptomatic for many years. Among the asymptomatic patients with preserved LV systolic function the risk of death is about 1%, but increases significantly when symptoms occur. Deterioration of the left …