(IV-5A.2) (English) Patient after correction of Tetralogy of Fallot with pulmonary valve regurgitation and left pulmonary branch stenosis Tomkiewicz-Pająk L. MD, PhD, Podolec J. MD, Kopeć G. MD, PhD, Drabik L. MD, Assoc. Prof. Olszowska M. MD, PhD, Miszalski-Jamka T. MD, PhD, Assoc. Prof. Kostkiewicz M. MD, PhD, Tyrka A. MD
Keywords: correction of Tetralogy, pulmonary valve regurgitation, left pulmonary branch stenosis Background Tetralogy of Fallot (ToF) is a cyanotic congenital heart disease. Almost all unoperated patients used to die before 40 years of age. Prognosis after surgical correction is good, with a 35-year survival of 85%. Surgery is carried out to close ventricular septal defect and relieve right ventricular outflow tract obstruction. Patients who have reached adulthood after earlier repair of ToF frequently develop complications such as severe pulmonary regurgitation, …
(IV-1D.1b) (English) Ebstein’s anomaly with bidirectional shunt through ASD Klima L., Dziedzic H., Rajzer M., Olszanecka A., Czarnecka D.
Keywords: Ebstein’s anomaly, bidirectional shunt, ASD Background Ebstein’s anomaly is a congenital heart defect that appears in 1 on 100 000 to 200 000 births. In this defect tricuspid valve is dislocated towards the apex of the right ventricle. The annulus of the valve is in the standard position and leaflets are attached to the walls and septum of the right ventricle. This leads to atrialization of a portion of the right ventricle. The right atrium is enlarged and the …
(IV-2A.1) (English) 18-year-old patient with tetralogy of Fallot and coronary artery abnormality Smaś-Suska M.MD, Tomkiewicz-Pająk L. MD,PhD, Tyrka A. MD, Olszowska M. MD, PhD, Miszalski-Jamka T. MD, PhD, Podolec J. MD
Keywords: coronary artery abnormality, tetralogy of Fallot Background Tetralogy of Fallot is one of the most common cyanotic congenital cardiac diseases. This heart defect consists of ventricular septal defect, obstruction of the right ventricular outflow tract, overriding aorta and right ventricular hypertrophy. About 3% of patients have anomalous left anterior descending coronary artery which may necessitate a conduit type of repair. Conduits connect right ventricle and main pulmonary artery. There are two types of conduits: valved and non-valved. About 40% …
(IV-2B.1) (English) A 69 year old woman with atrial septal defect, coronary heart disease and pulmonary arterial hypertension Rozenbergs A.
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(IV-3A) Adult patient after Fontan procedure with heterotaxy syndrome, vena cava inferior – pulmonary artery tunnel narrowing Tomkiewicz-Pająk L., Miszalski-Jamka T., Krupiński M., Banyś P., Olszowska M., Podolec M., Drabik L., Podolec P.
Experts: Janusz Skalski J., Jacek Kołcz J., Trojnarska O., Kopeć G., Miszalski- Jamka T.
Background Heterotaxy syndrome is a rare defect that involves the heart and other organs. It is a disorder that results in certain organs forming on the opposite side of the body. The incidence of typical forms is 2,5/100 000 births. Heterotaxy coming from greek word “heteros” meaning different and “taxis” meaning arrangement. These malformations are always associated with additional cardiac lesions such as univentricular heart (UV). The Fontan operation was introduced in 1968 and has become the definitive treatment for …
(IV-5A.O) (English) Adult patient after correction of tetralogy of Fallot with a single branch of the pulmonary artery Tomkiewicz-Pająk L., Drabik L., Krupiński M., Podolec J., Banyś P., Rubiś P., Podolec P.
Experts: Skalski J., Pająk J., Trojnarska O., Gąsior Z., Miszalski – Jamka T.
Background Tetralogy of Fallot is a rare congenital cardiac diseases occurring in one of every 35,0000-30,000 live births. This malformation consists of ventricular septal defect, obstruction of the right ventricular outflow tract, override of the ventricular septum by the aortic root, and in consequence right ventricular hypertrophy. It is the most common cyanotic heart defect. Abnormalities of the pulmonary arteries following palliative or corrective surgery for tetralogy of Fallot (TOF) are common. There are only a few written cases of …
(IV-6.O) 59-year-old female with patent foramen ovale (PFO) and persistent atrial fibrillation as a potential cause of recurrent cerebral ischemic events Komar M., Podolec J., Przewłocki T., Sobień B., Tomkiewicz-Pająk L., Motyl R., Kopeć G.
Experts: Przewłocki T., Małecka B., Kopeć G., Podolec P.
Background Patent foramen ovale (PFO) occurs in 25% of healthy adults. Several pathologies are related to PFO including paradoxical embolism, migraine with aura and decompression illness in divers. Finding a PFO in patients suffering a stroke and/or TIA is common in daily practice. Therapeutic approach in such cases is complex and often controversial. Treatment options consist of antiplatelet therapy with aspirin, oral anticoagulation with VKA or percutaneous defect closure. The authors present a case of patient suffering a TIA, with …
(IV-1C.3b) 21-year-old male with Truncus Arteriosus Type I Komar M. , Wilkołek P. , Kopeć G. , Sobień B. , Stępniewski J. , Tyrka A., Widlińska B., Podolec P.
Experts: Skalski J., Pająk J., Olszowska M., Tomkiewicz- Pająk L.
Background Truncus arteriosus communis (TAC) is a rare congenital heart disease appearing in 0.034 to 0.56 per 1,000 newborns and representing 1.4% to 2.8% of all cases of congenital heart diseases. In this anomaly, a single arterial trunk arises from the heart, overrides the interventricular septum, and supplies systemic, pulmonary, and coronary circulations. Without surgical treatment, 80% of patients die within the first year of life, usually in early infancy. Repair of TAC during the neonatal and early infant period …
(IV-2B.3) 66-year-old female with perimembranous ventricular septal defect (VSD) Luszczak J., Tomkiewicz- Pajak L., Olszowska M., Sutor U., Podolec P., Prokop-Staszecka A.
Experts: Fijałkowska A., Trojnarska O., Skalski J., Gąsior Z., Rubiś P., Kopeć G., Podolec P.
Background Ventricular septal defect (VSD) is the most common congenital heart anomaly. The most frequent location is the membranous septum. The volume and direction of the shunt depends on the size of the VSD, pulmonary vascular resistance (PVR) and the right and left ventricular function. Adult patients with VSD are often after surgical treatment in childhood. Untreated patients may have small VSD with left-right shunt, without LV overload and pulmonary hypertension (PH); VSD with left-right shunt and PH or VSD …