1. Pulmonary hypertension in a patient with congenital shunt and left ventricular dysfunction

Keywords: Eisenmenger syndrome, Pulmonary Capillary Wedge Pressure, Down syndrome Background Pulmonary hypertension (PH) is a hemodynamic and pathophysiological condition defined as an increase in mean pulmonary arterial pressure (PAP)≥ 25 mmHg at rest as assessed by right heart catheterization. PH can be found in multiple clinical conditions. Complete atrioventricular canal (CAVC), an uncommon CHD often associated with Down syndrome, is characterised by an ostium primum atrial septal defect, a common atrioventricular valve and a variable deficiency of the ventricular septum …