(I-1B.3) Vascular ring in adult patient Prof. Grażyna Bochenek MD, PhD Marek Przybyszowski MD, PhD
BRIEF COMMENTS EXPERT: Prof. Grażyna Bochenek, MD, PhD Affiliation: Department of Pulmonology, Jegiellonian University, Krakow, Poland COMMENT It is difficult to evaluate direct association between severity of asthma and coexisting vascular ring. There is a positive allergic history. Due to the esophagus compression, the patient has difficulties with swallowing. Chocking with food can increase bronchi reactivity. Currently pulmonologic management is being optimized. EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, …
(I-1B.3) Adult patient with vascular ring Lidia Tomkiewicz-Pająk MD PhD, Natalia Dłużniewska MD, Leszek Drabik MD PhD, Prof Maria Olszowska MD, PhD, Prof Piotr Podolec MD PhD
Experts: Prof Piotr Pieniążek MD PhD, Jacek Pajak MD PhD, Anna Prokop-Staszecka Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Roland Hetzer, MD PhD, cardiac surgeon Affiliation: Deutsches Herzzentrum, Berlin, Germany COMMENT This rare condition is called arteria subclavia lusoria. It may cause stridor due to compression. Dilated proximal segment of descending aorta – so called Diverticulum, is the place where the aneurysm develops. Obstruction of trachea might in this case be caused as well by Diverticulum not artery itself. Operation should be performed: reduction of Diverticulum and transposition of artery to the proper position. …
(I-1B.3) Adult patient with vascular ring Prof. Piotr Podolec MD, PhD, Lidia Tomkiewicz-Pająk MD, PhD, Leszek Drabik MD, Henryk Olechnowicz MD PhD, Prof. Maria Olszowska MD, PhD
Background Vascular ring is rare congenital malformation, it accounts for less than 1% of all congenital heart problems. The condition occurs as often in males as females. Some infants with vascular ring also have another congenital heart problem. With vascular ring, some of the arches and vessels that should have changed into arteries or disappeared are still present when the baby is born. The primary symptomatology associated with vascular rings relates to the structures that are encircled by the ring, …
(I-1B.6) Adult patient with coarctation of the aorta Lidia Tomkiewicz-Pająk MD, PhD, Justyna Błaut-Jurkowska MD , Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD, Prof. Tadeusz Przewłocki MD, PhD, Jakub Stpniewski MD, PhD
Background Coarctation of the aorta accounts for 5–8% of all congenital heart defects. The male-to-female ratio is 2:1. It is defined as a narrowing of the aorta, typically located in the area where the ductus arteriosus inserts.Coarctation of the aorta may occur as an isolated form or in association with various other cardiac and non-cardiac lesions. Signs and symptoms depend on the severity of CoA. Patients with serious CoA exhibit signs and symptoms early in life, while particularly mild cases …
(I-1B.6) 33 year-old patient with coarctation of the aorta and tetralogy of Fallot Lidia Tomkiewicz-Pająk, Tomasz Pawelec
Background Tetralogy of Fallot (TOF) is one of the most common congenital heart development disorders (CHDs). This condition is classified as cyanotic heart disorder. It consists of right ventricular (RV) outflow tract obstruction (RVOTO) (infundibular stenosis), ventricular septal defect (VSD), aorta dextroposition, and right ventricular hypertrophy. Patients with tetralogy of Fallot initially present with cyanosis shortly after birth, thereby attracting early medical attention. Surgical correction is a procedure of choice. It is usually performed in the infancy. Sometimes reoperations are …
(I-1B.6) Adult patient with coarctation of the aorta (CoA) Danuta Sorysz MD. PhD, Barbara Zawiślak MD
Background Coarctation of aorta is a common congenital malformation that is usually treated in childhood. Adult patient with CoA have a important incidence of associated cardiac disorders include bicuspide aortic valve (up to 85%), parachute mitral valve and atrial fibrillation, ischemic heart disease. Clinical features include upper body systolic hypertension, lower body hypotension, a blood pressure gradient between upper and lower extremities (20 mmHg indicates significant CoA), radiofemoral pulse delay. Diagnostic methods are echocardiography, CT, NMR, angiography. In case of …