(II-1A.5) 41-year-old patient with chronic thromboembolic pulmonary hypertension Marcin Waligóra MD, Agnieszka Sarnecka MD, Grzegorz Kopeć MD, PhD, Prof. Piotr Podolec MD, PhD

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Background Acute pulmonary embolism is rarely complicated by development of pulmonary hypertension (PH) with estimated incidence rate of 0,5-2%. It is almost impossible to determine the overall prevalence of chronic thromboembolic pulmonary hypertension (CTEPH) since not all of these patients have a history of acute pulmonary embolism. For patients after acute pulmonary embolism, diagnosis can be made after 3 months of effective anticoagulation, and remaining signs of PH. Final diagnosis can be made after confirming pre-capillary PH during right heart …

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(II-1A.5) A 39-year-old woman with atypical variant of Klippel-Trenaunay syndrome and progressive thromboembolic pulmonary hypertension, successfully treated by pulmonary thromboendarterectomy Poręba M, Misztal M, Biederman A, Skrzypek A, Szatkowski P, Pirsztuk E, Czernecka-Mroczek D, Gackowski A , Nessler J

Background Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular malformation of veins, capillaries and lymphatic vessels which can be associated with thromboembolic events. We report on a female with severely complicated course of the disease. Case presentation We present a case of 39-year-old female with Klippel-Trenaunay syndrome (KTS) complicated by deep vein thrombosis and chronic thromboembolic pulmonary hypertension (CTEPH). Our patient was operated in adolescence and severe varicosities of her lower limb were excised. After second pregnancy she developed pulmonary …

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(II-1A.5) Chronic thromboembolic pulmonary hypertension Skaidrius MiliauskasMD, PhD, Deimante Hoppenot MD, PhD

Background Chronic thromboembolic pulmonary hypertension (CTEPH) is a life-threatening condition in which organised thrombi obstruct the pulmonary vessels, causing increased pulmonary vascular resistance, progressive pulmonary hypertension (PH) and right heart failure. CTEPH is associated with considerable morbidity and mortalities. Even if more recent papers suggest that the prevalence of CTEPH is up to 3.8% in survivors of acute pulmonary embolism, most experts believe that the true incidence of CTEPH after acute pulmonary embolism is 0.5–2%. CTEPH can be found in …

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(II-1A.5) 27- year old male with pulmonary hypertension and pate Andris Skride, MD

Expert’s conclusions: The patient should undergo pulmonary thromboendarterectomy. Authors: Andris Skride, MD1 1 Pauls Stradins Clinical University Hospital Latvian Cardiology Center   case presentations and videos are provided for private use only

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