(II-3B.1) Pulmonary artery aneurysm in a patient with Eisenmenger’s syndrome Mroczek Ewa1, Furdal Michał1, Jakub Stępniewski2
Background Eisenmenger syndrome is a clinical condition, in which congenital heart defect (CHD) with persistent intracardiac shunt results in development of pulmonary hypertension. With time right-to-left shunt becomes reversed leading to development of cyanosis. Eisenmenger s. may be caused by a number of different CHDs including various forms of ventricular or atrial septal defects, patent ductus arteriosus, aortopulmonary window etc. or as a result of surgical correction of CHDs with formation of systemic-to-pulmonary shunts. The overall prognosis for Eisenmenger patients …
(II-1A.5) A 39-year-old woman with atypical variant of Klippel-Trenaunay syndrome and progressive thromboembolic pulmonary hypertension, successfully treated by pulmonary thromboendarterectomy Poręba M, Misztal M, Biederman A, Skrzypek A, Szatkowski P, Pirsztuk E, Czernecka-Mroczek D, Gackowski A , Nessler J
Background Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular malformation of veins, capillaries and lymphatic vessels which can be associated with thromboembolic events. We report on a female with severely complicated course of the disease. Case presentation We present a case of 39-year-old female with Klippel-Trenaunay syndrome (KTS) complicated by deep vein thrombosis and chronic thromboembolic pulmonary hypertension (CTEPH). Our patient was operated in adolescence and severe varicosities of her lower limb were excised. After second pregnancy she developed pulmonary …
(II-1A.4d) 47 years old female with Patent Ductus Arteriosus and Pulmonary Hypertension. Jakub Stępniewski MD, Grzegorz Kopeć MD, PhD, Hanna Dziedzic-Oleksy MD, Anna Tyrka MD, Prof. Piotr Podolec MD, PhD
Background Ductus arteriosus (DA) is a vascular connection between the main pulmonary artery and the aorta that allows blood to bypass the fetus’s non-functioning lungs. After delivery, the DA undergoes active constriction and obliteration eventually. A patent ductus arteriosus (PDA) occurs when the DA fails to close postnatally. PDA is an uncommon clinical finding in adult population. Improvement of survival of premature infants at risk for PDA and an increase in cases discovered incidentally, the incidence of PDA is rising …
(II-1A.4d) Patient with ventricular septal defect and Eisenmenger syndrome with gynecological complications Magdalena Kaźnica-Wiatr MD, Magdalena Nowacka MD, Grzegorz Kopeć MD, PhD, Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
Background Eisenmenger syndrome is defined as pulmonary vascular obstructive disease which develops as a consequence of preexisting large left-to-right shunt such that pulmonary artery pressures approach systemic values and the direction of the flow becomes bidirectional or right-to-left. Congenital heart defects that can lead to Eisenmenger syndrome include “simple” defects like ASD, VSD, PDA or “complex” like AVSD, truncus arteriosus, aortopulmonary window and univentricular heart. Elevated pulmonary vascular resistance usually occurs in infancy, by the age of 2 years. Clinical …
(II-1A.5) Chronic thromboembolic pulmonary hypertension Skaidrius MiliauskasMD, PhD, Deimante Hoppenot MD, PhD
Background Chronic thromboembolic pulmonary hypertension (CTEPH) is a life-threatening condition in which organised thrombi obstruct the pulmonary vessels, causing increased pulmonary vascular resistance, progressive pulmonary hypertension (PH) and right heart failure. CTEPH is associated with considerable morbidity and mortalities. Even if more recent papers suggest that the prevalence of CTEPH is up to 3.8% in survivors of acute pulmonary embolism, most experts believe that the true incidence of CTEPH after acute pulmonary embolism is 0.5–2%. CTEPH can be found in …
(VII- II-1A.4d) Pregnancy in a patient with Eisenmenger syndrome Ewa Mroczek
Authors: Ewa Mroczek1 1Cardiology department Regional Hospital in Wrocław Research and Development Centre case presentations and videos are provided for private use only
(II-1A.5) 27- year old male with pulmonary hypertension and pate Andris Skride, MD
Expert’s conclusions: The patient should undergo pulmonary thromboendarterectomy. Authors: Andris Skride, MD1 1 Pauls Stradins Clinical University Hospital Latvian Cardiology Center case presentations and videos are provided for private use only
(II-1C.1) 23-year-old man with Down syndrome, complete AV canal, Eisenmenger syndrome, and elevated Pulmonary Capillary Wedge Pressure (PCWP) Kopeć G., Stępniewski J., Tyrka A.,
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Keywords: Eisenmenger syndrome, Pulmonary Capillary Wedge Pressure, Down syndrome Background Pulmonary hypertension (PH) is a hemodynamic and pathophysiological condition defined as an increase in mean pulmonary arterial pressure (PAP)≥ 25 mmHg at rest as assessed by right heart catheterization. PH can be found in multiple clinical conditions. Complete atrioventricular canal (CAVC), an uncommon CHD often associated with Down syndrome, is characterised by an ostium primum atrial septal defect, a common atrioventricular valve and a variable deficiency of the ventricular septum …
(II-1C.2) Patient with atrial septal defect pulmonary embolism and pulmonary hypertension Podolec M., Kopeć G., Tytka A.
Experts: Lang I.
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case presentations and videos are provided for private use only
(II-1A.4d) 62-year-old female with Ostium Secundum Atrial Septal Defect (ASD t. II) and coexisting pulmonary hypertension Stepniewski J., Podolec M., Komar M., Wójtowicz M., Tyrka A., Nowacka M., Kopeć G., Rubiś P., Tomkiewicz-Pająk L.,
Experts: Sadowski J., Kapelak B., Podolec P.
Background Ostium Secundum Atrial Septal Defect (ASD II) is the most commonly diagnosed type of ASDs. It accounts for about 75% of all ASD cases, representing approximately 7% of all congenital cardiac defects and 30-40% of all congenital heart disease in patients older than 40 years. It is characterized by a defect in the interatrial septum allowing pulmonary venous return to pass directly from the left atrium to the right atrium. The condition can be left undiagnosed for many years …