( I – 2A.0; IV – 1D.2d ) Patient with artificial aortic valve with aneurysm of ascending aorta Natalia Dłużniewska MD; Lidia Tomkiewicz – Pająk MD, PhD; Aleksandra Lenart MD, Monika Smaś – Suska MD, Prof. Maria Olszowska MD, PhD; Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD, pediatric cardiac surgeon Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow, Poland COMMENT Ascending aorta’s diameter has shown widening tendency. It is difficult to determine if the implanted AV is still suitable for the patient. I recommend consideration of AVR procedure (for example implantation of biological valve and plasty of the ascending aorta). Bioprothesis might improve the patient’s quality of life. Aortic homograft implantation would make possible …
Posted in 1. Abnormalities of the position and connection of the heart and vessels, 2. Connective tissue disorders causing aneurysmal disease, 2. Left heart valves, A. Aneurysmal disease of the aorta, Case presentations, D. Valves, I. Rare diseases of systemic circulation, IV. Rare congenital cardiovascular diseases, Others
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(I-1C.O) 57-year-old patient with a coronary arteries anomaly Monika Smaś-Suska MD, Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Piotr Musiałek MD, PhD, Natalia Dłużniewska MD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
EXPERTISE 1 EXPERTISE 2 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(I-1C.4) Overlap cardiomyopathy – coexistence of hypertrophic and restrictive cardiomyopathy phenotypes in one patient Sylwia Wiśniowska-Śmałek MD, Paweł Rubiś MD, PhD, Monika Dzieciuch- Rojek, Dawid Kudliński MD, Agata Leśniak-Sobelga MD, PhD, Magdalena Kostkiewicz MD, PhD Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Roland Hetzer, MD, PhD Affiliation: German Heart Instiute, Berlin, Germany COMMENT Considering clinical data and results of the medical tests the patient is likely a future heart transplantation candidate. No relevant ventricular arrhythmias were detected and I would not recommend ICD implantation. However due to coexistent scoliosis the patient should undergo lung function tests and pulmonological consultation to plan the best possible post-op management. The scoliosis itself is not a contraindication to HTx. EXPERT: Assoc. …
(I-1B.3) Vascular ring in adult patient Prof. Grażyna Bochenek MD, PhD Marek Przybyszowski MD, PhD
BRIEF COMMENTS EXPERT: Prof. Grażyna Bochenek, MD, PhD Affiliation: Department of Pulmonology, Jegiellonian University, Krakow, Poland COMMENT It is difficult to evaluate direct association between severity of asthma and coexisting vascular ring. There is a positive allergic history. Due to the esophagus compression, the patient has difficulties with swallowing. Chocking with food can increase bronchi reactivity. Currently pulmonologic management is being optimized. EXPERT: Assoc. Prof. Jacek Kołcz, MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, …
(I-3A.1) Rheumatic heart disease and Takayasu’s arteritis. Can these two diseases coexist? Prof. Egle Ereminiene MD, PhD, Cardiologist Raimonda Verseckaite, Cardiology resident Laura Urbonaite
BRIEF COMMENTS EXPERT: Prof. Roland Hetzer, MD, PhD Affiliation: German Heart Instiute, Berlin, Germany COMMENT Considering the current symptoms, impairment of exercise tolerance is most probably the result of mitral regurgitation, rather than peripheral artery disease. Mitral valve replacement is recommended. EXPERT: Paweł Rubiś, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT Coexistence of two diseases (atherosclerosis and vasculitis) cannot be excluded. However, there are no signs of active inflammatory process …
(II-1C.O) What is the coincidence of pulmonary arterial hypertension associated with congenital cardiac shunt and hypertrophic cardiomyopathy in patient with trisomy 21 Wojciech Wróbel MD, PhD, Prof.Katarzyna Mizia-Stec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Medical College, Krakow COMMENT Diagnosis of cardiomyopathy needs closer evaluation. Ventricular hypertrophy and pulmonary arterial hypertension might be consequences of congenital heart defect, not necessarily cardiomyopathy. It is not clear why the patient wasn’t operated in the past? EXPERT: Prof. Katarzyna Mizia-Stec MD, PhD Affiliation: 1st Department of Cardiology, Medical University of Silesia, Katowice,Poland COMMENT Ventricle hypertrophy was first noticed in 2005. Question …
(I-1C.4) 44-year-old patient with anomalous circumflex artery shunt to the right atrium and moderate mitral regurgitation Podolec J. MD PhD, Nosal M. MD, Górkiewicz-Kot I. MD PhD, Sobczyk D. MD PhD, Kopec G. MD, PhD, prof. Sadowski J. MD, PhD, prof. Zmudka K. MD, PhD
BRIEF COMMENTS EXPERT: Prof. Henryk Siniawski MD, PhD Affiliation: Deutsches Herzzentrum, Berlin, Germany COMMENT Surgery seems essential – it’s young patient with large ischemic area and LV dilatation. He has limited quality of life. Perhaps microreconstruction might be feasible. In case of patients disagreement for surgical treatment, I suggest exercise test 3 times a year – positive test with chest pain may motivate patient to agree for the operation.. Mitral regurgitation may have ischemic origin and may progress very …
(I-O) Multilevel atherosclerosis in 56 years old famale dr n. med. Hanna Dziedzic-Oleksy dr n. med. Monika Komar dr n. med. Łukasz Tekieli prof. dr hab. med. Piotr Pieniążek prof. dr hab. med. Piotr Podolec
BRIEF COMMENTS EXPERT: Prof. Egle Ereminiene MD, PhD Affiliation: Hospital of Lithuanian University of Health Sciences, Kaunas COMMENT At this point further conservative treatment seems the right choice. After intervention on carotid artery clopidogrel should be administered. Scintigraphy is essential to estimate ischemic region in the heart. Considering peripheral artery disease – exercise training aimed at improving the walking distance is necessary. Cilostazol do not improve prognosis, only symptoms, but our experience with this treatment is limited. EXPERT: Prof. …
(I-3A.5)19 YEAR OLD MALE WITH KAWASAKI DISEASE (KD) Hospital of Lithuanian University of Health Sciences Kaunas Clinics - department of Cardiology
Experts: prof. E. Ereminienė; prof. A. Baranauskaitė; res. R. Ordienė.
Brief Comments and Conclusion EXPERTISE 1 EXPERTISE 2 EXPERTISE 3
(I-1B.3) Adult patient with vascular ring Lidia Tomkiewicz-Pająk MD PhD, Natalia Dłużniewska MD, Leszek Drabik MD PhD, Prof Maria Olszowska MD, PhD, Prof Piotr Podolec MD PhD
Experts: Prof Piotr Pieniążek MD PhD, Jacek Pajak MD PhD, Anna Prokop-Staszecka Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Roland Hetzer, MD PhD, cardiac surgeon Affiliation: Deutsches Herzzentrum, Berlin, Germany COMMENT This rare condition is called arteria subclavia lusoria. It may cause stridor due to compression. Dilated proximal segment of descending aorta – so called Diverticulum, is the place where the aneurysm develops. Obstruction of trachea might in this case be caused as well by Diverticulum not artery itself. Operation should be performed: reduction of Diverticulum and transposition of artery to the proper position. …