(IV-5B.1) Heart failure in Fontan patient Lidia Tomkiewicz-Pająk, Monika Smaś –Suska, Maria Olszowska, Wojciech Płazak, Piotr Podolec
EXPERTISE 1 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1) 31-year old patient after Fontan operation with systemic AV valve regurgitation Knap K. MD, Tomkiewicz- Pająk L. MD, PhD, Prof. Olszowska M. MD, PhD, Prof. Podolec P. MD, PhD, Smaś- Suska M. MD, Jurkowska- Błaut J. MD
EXPERTISE 1 EXPERTISE 2 EXPERTISE 3 “Development of the European Network in Orphan Cardiovascular Diseases” “Rozszerzenie Europejskiej Sieci Współpracy ds. Sierocych Chorób Kardiologicznych”
(IV-5B.1 ) Patient with congenital heart disease – TGA, hypoplasia of right ventricle, left atrioventricular valve atresia and VSD Lidia Tomkiewicz-Pająk MD, PhD, Assoc. Prof. Maria Olszowska MD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Grzegorz Kopeć, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT There are no sufficient evidence from clinical trials for the use of sildenafil in presented case. EXPERT: Lidia Tomkiewicz-Pająk, MD, PhD Affiliation: Department of Cardiac and Vascular Diseases, John Paul II Hospital, Krakow, Poland COMMENT In current literature there are no data for beneficial influence of sildenafil in presented clinical situation. CONCLUSIONS 1. Psychological care indicated. 2. Cardiostimulator …
(IV-5A.O) Patient with coarctation of the aorta and Tetralogy of Fallot with significant pulmonary valve regurgitation Lidia Tomkiewicz-Pająk MD, PhD, Tomasz Pawelec MD, PhD, Natalia Dłużniewska MD, Grzegorz Kopeć MD, PhD, Paweł Rubiś MD, PhD, Prof. Maria Olszowska MD, PhD, Prof. Piotr Podolec MD, PhD
BRIEF COMMENTS EXPERT: Prof. Janusz Skalski MD, PhD Affiliation: Department of Pediatric Cardiac Surgery, Jagiellonian University Children’s Hospital, Krakow, Poland COMMENT Coexistence of Tetralogy of Fallot and coarctation of aorta is embriologically doubtful. Iatrogenic origin of the CoA should be taken under consideration. It might have also been a combination of VSD with pulmonary valve stenosis and coarctation of aorta as the primary defect. CONCLUSIONS 1) Percutaneous repair of pulmonary regurgitation should be taken under consideration EXPERTISE 1 …
(IV-5B.1) Patient after Fontan operation Mroczek E. MD, PhD, Podolec J. MD, Kusa J. MD, PhD
Keywords: Fontan operation Background Tricuspid atresia accounts for about 0.7% of all congenital heart diseases. The tricuspid valve is absent, and there is no anatomic connection and direct communication between the right atrium and the right ventricle. Case description This 27-year-old female after Fontan operation is presented. The patient was born at term but was cyanotic. Diagnosis was made of tricuspid atresia with atrial septal defect (ASD) and ventricular septal defect (VSD). At age of 3.5 years a Fontan circulation …