B. Complex abnormalities of position and connection of the heart and vessels with shunts

  BRIEF COMMENTS EXPERT: Prof. Henryk Siniawski MD, PhD, cardiac surgeon Affiliation: German Heart Instiute, Berlin, Germany COMMENT I would recommend RHC in order to exclude pulmonary hypertension. Optimal medical treatment is necessary to protect the patient form cardiac decompensation in the future. EXPERT: Assoc. Prof. Jacek Pająk, MD, PhD, pediatric cardiac surgeon Affiliation: Silesian Center for Heart Diseases, Zabrze, Poland COMMENT It appears that conservative treatment and watchful observation would be the most reasonable proceeding. EXPERT: Assoc. Prof. Jacek …

Background Nowadays we can observe increasing number of grown-up congenital heart diseases, due to remarkable improvement in survival of pediatrics patients. Most of adult patients have undergone palliative operation in first years of life. Patients with univentricular heart present a multiple variety of malformations: missing or hypoplastic left or right ventricle, connected with corresponding valvular and great vessels anomalies. In such cases, most patients have restricted pulmonary blood flow, palliatively treated in childhood by surgically made systemic-to-pulmonary shunts. Examples of …

Background Transposition of the great vessels is a congenital cyanotic heart defect. The hallmark of transposition of the great arteries is ventriculoarterial discordance, in which the aorta arises from the morphologic right ventricle and the pulmonary artery arises from the morphologic left ventricle. The Rastelli operation is performed for the repair of d-transposition of the great vessels with ventricular septal defect and pulmonary stenosis. During the surgery right ventricular outflow truckt – pulmonary arteries conduit is implanted and VSD is …